Familial infantile myoclonic epilepsy

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:352582OMIM:617976G40.3
Who is this for?
Show terms as
8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Familial infantile myoclonic epilepsy (FIME) is a very rare genetic seizure disorder that begins in infancy. Babies with this condition develop myoclonic seizures, which are brief, sudden jerking movements of the muscles. These seizures typically start within the first year or two of life. The condition runs in families, meaning it is passed down from parents to children through their genes. The myoclonic jerks can affect different parts of the body, including the arms, legs, or the whole body. They may happen many times a day and can be triggered by things like being startled, falling asleep, or waking up. Some children with this condition may also develop other types of seizures over time. Depending on the severity, the seizures can interfere with normal development, including motor skills and learning. Treatment mainly focuses on controlling seizures with anti-seizure medications (also called antiepileptic drugs). The response to medication can vary from child to child. Some children respond well to treatment and have good seizure control, while others may be harder to treat. Early diagnosis and treatment are important to give children the best chance at normal development. Because this is a rare condition, management is best handled by a team of specialists experienced in pediatric epilepsy.

Also known as:

Key symptoms:

Sudden brief muscle jerks (myoclonic seizures)Jerking of the arms or legsWhole-body jerking episodesSeizures triggered by being startledSeizures occurring when falling asleep or waking upPossible developmental delaysDifficulty with motor skillsPossible learning difficultiesEpisodes of staring or unresponsivenessFrequent falls due to sudden muscle jerks

Clinical phenotype terms (25)— hover any for plain English
Thick cerebral cortexHP:0006891Simple febrile seizureHP:0011171EEG with focal spike wavesHP:0011197Bilateral tonic-clonic seizure with generalized onsetHP:0025190Interictal EEG abnormalityHP:0025373
Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Infantile

Begins in infancy, roughly 1 month to 2 years old

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Familial infantile myoclonic epilepsy.

View clinical trials →

No actively recruiting trials found for Familial infantile myoclonic epilepsy at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Familial infantile myoclonic epilepsy community →

No specialists are currently listed for Familial infantile myoclonic epilepsy.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Familial infantile myoclonic epilepsy.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Familial infantile myoclonic epilepsyForum →

No community posts yet. Be the first to share your experience with Familial infantile myoclonic epilepsy.

Start the conversation →

Latest news about Familial infantile myoclonic epilepsy

No recent news articles for Familial infantile myoclonic epilepsy.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What type of seizures does my child have, and how does this specific diagnosis differ from other forms of epilepsy?,Which anti-seizure medication do you recommend, and what are the possible side effects?,Should my child have genetic testing, and what will the results tell us?,What should I do if my child has a prolonged seizure or a cluster of seizures?,Will this condition affect my child's development, and what therapies might help?,Is there a risk that my other children or future children could have this condition?,Are there any clinical trials or new treatments being studied for this condition?

Common questions about Familial infantile myoclonic epilepsy

What is Familial infantile myoclonic epilepsy?

Familial infantile myoclonic epilepsy (FIME) is a very rare genetic seizure disorder that begins in infancy. Babies with this condition develop myoclonic seizures, which are brief, sudden jerking movements of the muscles. These seizures typically start within the first year or two of life. The condition runs in families, meaning it is passed down from parents to children through their genes. The myoclonic jerks can affect different parts of the body, including the arms, legs, or the whole body. They may happen many times a day and can be triggered by things like being startled, falling asleep

How is Familial infantile myoclonic epilepsy inherited?

Familial infantile myoclonic epilepsy follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Familial infantile myoclonic epilepsy typically begin?

Typical onset of Familial infantile myoclonic epilepsy is infantile. Age of onset can vary across affected individuals.