Familial episodic pain syndrome

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ORPHA:391384OMIM:615040M79.6
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Overview

Familial episodic pain syndrome (FEPS) is a rare inherited condition that causes repeated episodes of intense pain, most commonly affecting the upper body, arms, and legs. The pain episodes typically begin in infancy or early childhood and can be triggered by factors such as fatigue, cold weather, fasting, or illness. During an episode, a person may experience severe pain in the joints, muscles, or other parts of the body that can last from minutes to days. Some forms of the condition also involve sweating, skin flushing, or other symptoms during pain attacks. The condition is caused by mutations in genes that affect how nerve cells sense and transmit pain signals. These genes are involved in sodium or other ion channels, which are tiny gateways in nerve cells that control electrical signals. When these channels do not work properly, the nerves can become overly sensitive and fire pain signals when they normally would not. There are several subtypes of familial episodic pain syndrome (FEPS1, FEPS2, FEPS3), each linked to a different gene. Treatment is mainly focused on managing pain during episodes. Some patients respond to common pain medications, while others may benefit from specific drugs that target the affected ion channels. There is currently no cure, but many patients find that episodes become less frequent or less severe as they get older.

Also known as:

Key symptoms:

Episodes of severe pain in the arms and legsPain in the upper body, chest, or abdomen during episodesJoint pain during flare-upsSweating during pain episodesSkin flushing or redness during attacksPain triggered by cold weather or temperature changesPain triggered by fatigue or physical stressPain triggered by fasting or not eatingPain triggered by illness or infectionEpisodes that start in infancy or early childhoodPain that comes and goes with symptom-free periods in betweenMuscle stiffness or cramping during episodesDifficulty sleeping during pain episodes

Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Infantile

Begins in infancy, roughly 1 month to 2 years old

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Familial episodic pain syndrome.

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No actively recruiting trials found for Familial episodic pain syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Familial episodic pain syndrome community →

No specialists are currently listed for Familial episodic pain syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Familial episodic pain syndrome.

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Community

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Latest news about Familial episodic pain syndrome

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Which subtype of familial episodic pain syndrome does my child have, and which gene is affected?,What are the best medications to manage pain during episodes?,Are there specific triggers we should try to avoid?,Will the episodes get better as my child grows older?,Should other family members be tested for this condition?,Are there any clinical trials or new treatments being studied for this condition?,What should we do if pain becomes severe and does not respond to our usual medications?

Common questions about Familial episodic pain syndrome

What is Familial episodic pain syndrome?

Familial episodic pain syndrome (FEPS) is a rare inherited condition that causes repeated episodes of intense pain, most commonly affecting the upper body, arms, and legs. The pain episodes typically begin in infancy or early childhood and can be triggered by factors such as fatigue, cold weather, fasting, or illness. During an episode, a person may experience severe pain in the joints, muscles, or other parts of the body that can last from minutes to days. Some forms of the condition also involve sweating, skin flushing, or other symptoms during pain attacks. The condition is caused by mutat

How is Familial episodic pain syndrome inherited?

Familial episodic pain syndrome follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Familial episodic pain syndrome typically begin?

Typical onset of Familial episodic pain syndrome is infantile. Age of onset can vary across affected individuals.