Exostoses-anetodermia-brachydactyly type E syndrome

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:1962OMIM:133690Q87.5
Who is this for?
Show terms as
8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Exostoses-anetodermia-brachydactyly type E syndrome is an extremely rare genetic condition that affects multiple body systems. The syndrome combines three main features: exostoses (bony growths or bumps that develop on the surface of bones, especially near joints), anetodermia (areas of loose, wrinkled, or sac-like skin caused by loss of the elastic tissue in the skin), and brachydactyly type E (unusually short fingers and toes, particularly affecting the metacarpal and metatarsal bones in the hands and feet). Because this condition involves bones, skin, and skeletal development, it is considered a multi-system disorder. The syndrome was described in only a very small number of families in the medical literature, making it one of the rarest known genetic conditions. Affected individuals may notice bony lumps near their joints during childhood or adolescence, patches of soft or baggy skin, and noticeably short hands or feet. The bony growths can sometimes cause discomfort, limit joint movement, or press on nearby nerves. The skin changes are usually painless but can be cosmetically concerning. There is currently no cure for this syndrome. Treatment is focused on managing symptoms. Surgical removal of exostoses may be needed if they cause pain or functional problems. Dermatological care can help monitor the skin changes. Orthopedic follow-up is important for the skeletal abnormalities. Because so few cases have been reported, the full range of possible symptoms and the best treatment approaches are still being understood.

Key symptoms:

Bony bumps or growths near joints (exostoses)Loose, wrinkled, or baggy patches of skin (anetodermia)Unusually short fingersUnusually short toesShort hands or feetJoint stiffness or limited range of motionPain or discomfort near bony growthsCosmetically noticeable skin changesPossible nerve compression from bony growthsShort stature of certain bones in hands and feet

Clinical phenotype terms (5)— hover any for plain English
Multiple exostosesHP:0002762Type E brachydactylyHP:0005863
Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Childhood

Begins in childhood, roughly ages 1 to 12

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Exostoses-anetodermia-brachydactyly type E syndrome.

View clinical trials →

No actively recruiting trials found for Exostoses-anetodermia-brachydactyly type E syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Exostoses-anetodermia-brachydactyly type E syndrome community →

No specialists are currently listed for Exostoses-anetodermia-brachydactyly type E syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Exostoses-anetodermia-brachydactyly type E syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Exostoses-anetodermia-brachydactyly type E syndromeForum →

No community posts yet. Be the first to share your experience with Exostoses-anetodermia-brachydactyly type E syndrome.

Start the conversation →

Latest news about Exostoses-anetodermia-brachydactyly type E syndrome

No recent news articles for Exostoses-anetodermia-brachydactyly type E syndrome.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What monitoring schedule do you recommend for the bony growths?,Are there any signs I should watch for that would mean a bony growth needs to be removed?,Is genetic testing available that could help confirm the diagnosis or identify the cause?,What can be done to manage or improve the skin changes?,Will the short fingers or toes affect my child's hand or foot function over time?,Are there any activities my child should avoid to prevent injury to the bony growths?,Should other family members be evaluated for this condition?

Common questions about Exostoses-anetodermia-brachydactyly type E syndrome

What is Exostoses-anetodermia-brachydactyly type E syndrome?

Exostoses-anetodermia-brachydactyly type E syndrome is an extremely rare genetic condition that affects multiple body systems. The syndrome combines three main features: exostoses (bony growths or bumps that develop on the surface of bones, especially near joints), anetodermia (areas of loose, wrinkled, or sac-like skin caused by loss of the elastic tissue in the skin), and brachydactyly type E (unusually short fingers and toes, particularly affecting the metacarpal and metatarsal bones in the hands and feet). Because this condition involves bones, skin, and skeletal development, it is conside

How is Exostoses-anetodermia-brachydactyly type E syndrome inherited?

Exostoses-anetodermia-brachydactyly type E syndrome follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Exostoses-anetodermia-brachydactyly type E syndrome typically begin?

Typical onset of Exostoses-anetodermia-brachydactyly type E syndrome is childhood. Age of onset can vary across affected individuals.