Dysostosis

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ORPHA:364559
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22Specialists8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Dysostosis is a broad term used to describe a group of rare bone disorders where certain bones do not form properly during development. The Orphanet code 364559 refers to dysostosis as a category of skeletal malformations rather than a single specific disease. In dysostosis, the problem lies in how individual bones develop, which is different from conditions that affect the entire skeleton. The bones affected can vary widely depending on the specific type of dysostosis, and may include bones of the skull, face, spine, ribs, or limbs. People with dysostosis may notice differences in the shape or size of certain body parts, such as the face, hands, feet, or chest. Some forms are mild and cause mainly cosmetic concerns, while others can lead to significant functional problems like difficulty breathing, hearing loss, or limited movement. The severity depends on which bones are involved and how severely they are affected. Treatment for dysostosis is generally supportive and depends on the specific type and severity. Surgery may be needed to correct bone abnormalities, especially in the skull or face. Physical therapy, hearing aids, and other supportive measures can help manage symptoms. Genetic counseling is important for affected families, as many forms of dysostosis have a genetic basis. Research continues to better understand the underlying causes and develop improved treatments for these conditions.

Key symptoms:

Abnormal shape of the skullFacial bone differencesUnderdeveloped or missing bonesShort or malformed fingers or toesRib abnormalitiesHearing lossBreathing difficultiesAbnormal jaw developmentWidely spaced eyesCleft palateLimited joint movementShort statureSpinal abnormalitiesDental problems

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

FDA & Trial Timeline

6 events
Feb 2025Opioid Sparing Effect of an ISP Nerve Block on Post-Op Pain Control in Posterior Cervical Spine Surgery

Stony Brook University — NA

TrialRECRUITING
Feb 2022Fusion or no Fusion After Decompression of the Spinal Cord in Patients With Degenerative Cervical Myelopathy

Uppsala University Hospital — NA

TrialRECRUITING
Nov 2020Trigger Point Injections in Anterior Cervical Surgery

George Washington University — PHASE4

TrialRECRUITING
Mar 2020Study of Posterior Cervical Stabilization System (PCSS) as Part of Circumferential Fusion to Treat Multilevel DDD

Providence Medical Technology, Inc. — NA

TrialACTIVE NOT RECRUITING
Sep 2019Clinical and Radiological Outcomes of Posterior Cervical Fusion Supplemented With Interfacet Spacers

Ohio State University

TrialRECRUITING
Nov 2018Airway Management of Pediatric Patients With Klippel-Feil Syndrome

Boston Children's Hospital

TrialACTIVE NOT RECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Dysostosis.

View clinical trials →

No actively recruiting trials found for Dysostosis at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Dysostosis community →

Specialists

22 foundView all specialists →
AM
Ann Van Heest, MD
Specialist
PI on 1 active trial1 Dysostosis publication
SM
Susan Goobie, MD
BOSTON, MA
Specialist
PI on 1 active trial
PM
Paul S Kruszka, M.D.
CHARLOTTESVILLE, VA
Specialist
PI on 3 active trials
NM
Nicola Disma, MD
Specialist
PI on 1 active trial
MP
Matthew L Speltz, PhD
SEATTLE, WA
Specialist
PI on 1 active trial
CM
Carrie L Heike, MD, MS
SEATTLE, WA
Specialist
PI on 1 active trial
DP
Didier LACOMBE, PU-PH
Specialist
PI on 1 active trial
CM
Carrie Heike, MD, MS
SEATTLE, WA
Specialist
PI on 1 active trial
MP
Mark Sun, PhD
COON RAPIDS, MN
Specialist
PI on 1 active trial
FR
Federico DI ROCCO
Specialist
PI on 1 active trial19 Dysostosis publications
LM
Luis Féliz Vinas, MD
WEST PALM BEACH, FL
Specialist
PI on 1 active trial
LM
Luisa Veronese, MD
Specialist
PI on 1 active trial1 Dysostosis publication
LM
Luca Massimi
Specialist
PI on 1 active trial17 Dysostosis publications
RP
Rogerio Panizzutti, Professor
Specialist
PI on 1 active trial2 Dysostosis publications
PM
Patcharee Sriswasdi, MD, MPH
CHICAGO, IL
Specialist
PI on 1 active trial
JM
Jad G Khalil, MD
SOUTHFIELD, MI
Specialist
PI on 2 active trials
KP
Kimmo Lonnrot, MD, PhD
Specialist
PI on 1 active trial
SM
Sarkis Derderian, MD
COLUMBIA, SC
Specialist
PI on 1 active trial
NR
Norma Ab Rahman
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Dysostosis.

Search all travel grants →NORD Financial Assistance ↗

Community

Open DysostosisForum →

No community posts yet. Be the first to share your experience with Dysostosis.

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Latest news about Dysostosis

Disease timeline:

New recruiting trial: Trigger Point Injections in Anterior Cervical Surgery

A new clinical trial is recruiting patients for Dysostosis

New recruiting trial: Opioid Sparing Effect of an ISP Nerve Block on Post-Op Pain Control in Posterior Cervical Spine Surgery

A new clinical trial is recruiting patients for Dysostosis

New recruiting trial: Fusion or no Fusion After Decompression of the Spinal Cord in Patients With Degenerative Cervical Myelopathy

A new clinical trial is recruiting patients for Dysostosis

New recruiting trial: Clinical and Radiological Outcomes of Posterior Cervical Fusion Supplemented With Interfacet Spacers

A new clinical trial is recruiting patients for Dysostosis

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific type of dysostosis does my child have, and what gene is involved?,Which bones are affected, and how might this change as my child grows?,Will my child need surgery, and if so, when and what kind?,Should we have hearing and vision tested regularly?,What is the chance of this condition occurring again in future pregnancies?,Are there any complications we should watch for as my child develops?,Can you refer us to a specialized center with experience in this condition?

Common questions about Dysostosis

What is Dysostosis?

Dysostosis is a broad term used to describe a group of rare bone disorders where certain bones do not form properly during development. The Orphanet code 364559 refers to dysostosis as a category of skeletal malformations rather than a single specific disease. In dysostosis, the problem lies in how individual bones develop, which is different from conditions that affect the entire skeleton. The bones affected can vary widely depending on the specific type of dysostosis, and may include bones of the skull, face, spine, ribs, or limbs. People with dysostosis may notice differences in the shape

At what age does Dysostosis typically begin?

Typical onset of Dysostosis is neonatal. Age of onset can vary across affected individuals.

Which specialists treat Dysostosis?

22 specialists and care centers treating Dysostosis are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.