Dysmorphism-pectus carinatum-joint laxity syndrome

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Overview

Dysmorphism-pectus carinatum-joint laxity syndrome is an extremely rare genetic condition that affects the way the body develops, particularly the skeleton, joints, and facial features. The name describes its three main features: dysmorphism (unusual facial features), pectus carinatum (a chest that sticks out more than normal, sometimes called "pigeon chest"), and joint laxity (joints that are unusually loose and flexible, also called hypermobility). People with this condition may also have other skeletal differences, growth issues, and sometimes mild developmental delays. Because this syndrome is so rare, it has been described in only a very small number of individuals or families in the medical literature. The exact genetic cause has not been fully established, and much of what is known comes from detailed case reports. Facial features may include a broad forehead, widely spaced eyes, a flat nasal bridge, and other subtle differences that a trained geneticist can recognize. There is currently no cure for this condition. Treatment focuses on managing individual symptoms. For example, orthopedic care may be needed for the chest wall abnormality or joint problems, and physical therapy can help strengthen muscles around loose joints. Regular follow-up with a team of specialists is important to monitor growth and development and address any new concerns as they arise.

Also known as:

Key symptoms:

Chest that sticks out (pigeon chest or pectus carinatum)Unusually loose and flexible joints (joint hypermobility)Unusual facial featuresWidely spaced eyesBroad or prominent foreheadFlat nasal bridgeShort stature or growth delaysSkeletal abnormalitiesPossible mild developmental delayFrequent joint dislocations or sprainsLow muscle tone

Clinical phenotype terms (11)— hover any for plain English
Tented upper lip vermilionHP:0010804
Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Dysmorphism-pectus carinatum-joint laxity syndrome.

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No actively recruiting trials found for Dysmorphism-pectus carinatum-joint laxity syndrome at this time.

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No specialists are currently listed for Dysmorphism-pectus carinatum-joint laxity syndrome.

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Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Dysmorphism-pectus carinatum-joint laxity syndrome.

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Community

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Caregiver Resources

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Questions for your doctor

Bring these to your next appointment

  • Q1.What specific features does my child have that led to this diagnosis?,Should we pursue genetic testing such as whole exome sequencing to look for a cause?,What specialists should be part of our care team?,How can we best protect my child's joints during daily activities and sports?,Does the chest wall shape need treatment, and if so, when?,Are there any signs or symptoms we should watch for that would need urgent attention?,What developmental support services would you recommend?

Common questions about Dysmorphism-pectus carinatum-joint laxity syndrome

What is Dysmorphism-pectus carinatum-joint laxity syndrome?

Dysmorphism-pectus carinatum-joint laxity syndrome is an extremely rare genetic condition that affects the way the body develops, particularly the skeleton, joints, and facial features. The name describes its three main features: dysmorphism (unusual facial features), pectus carinatum (a chest that sticks out more than normal, sometimes called "pigeon chest"), and joint laxity (joints that are unusually loose and flexible, also called hypermobility). People with this condition may also have other skeletal differences, growth issues, and sometimes mild developmental delays. Because this syndro

At what age does Dysmorphism-pectus carinatum-joint laxity syndrome typically begin?

Typical onset of Dysmorphism-pectus carinatum-joint laxity syndrome is neonatal. Age of onset can vary across affected individuals.