Dysmorphism-cleft palate-loose skin syndrome

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ORPHA:1779Q87.0
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8Treatment centers

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Overview

Dysmorphism-cleft palate-loose skin syndrome is an extremely rare genetic condition that affects multiple parts of the body. It is sometimes referred to by its Orphanet designation (ORPHA:1779). The syndrome is characterized by a combination of unusual facial features (dysmorphism), an opening in the roof of the mouth (cleft palate), and abnormally loose or stretchy skin. Children born with this condition may also have growth delays, intellectual disability, and skeletal abnormalities. The loose skin can resemble conditions like cutis laxa, where the skin hangs in folds and lacks normal elasticity. Facial features may include a flat midface, widely spaced eyes, and a broad or flat nasal bridge. Because this syndrome is so rare, with very few cases described in the medical literature, the full range of symptoms and the underlying genetic cause are not yet completely understood. Treatment is supportive and focuses on managing individual symptoms. Surgical repair of the cleft palate is typically performed in infancy to help with feeding and speech development. Other therapies may include physical therapy, developmental support, and monitoring by multiple specialists. There is currently no cure or disease-specific treatment available.

Key symptoms:

Cleft palate (opening in the roof of the mouth)Loose or saggy skinUnusual facial featuresWidely spaced eyesFlat or broad nasal bridgeGrowth delay or short statureIntellectual disability or developmental delayJoint hypermobility (overly flexible joints)Skeletal abnormalitiesFeeding difficulties in infancySpeech delayLow muscle tone

Clinical phenotype terms (12)— hover any for plain English
Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Dysmorphism-cleft palate-loose skin syndrome.

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No actively recruiting trials found for Dysmorphism-cleft palate-loose skin syndrome at this time.

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No specialists are currently listed for Dysmorphism-cleft palate-loose skin syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Dysmorphism-cleft palate-loose skin syndrome.

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Community

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Caregiver Resources

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Mental Health Support

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Family & Caregiver Grants

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Social Security Disability

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Questions for your doctor

Bring these to your next appointment

  • Q1.What specific features does my child have that led to this diagnosis?,Should we pursue genetic testing such as whole exome sequencing to confirm the diagnosis?,When should cleft palate repair surgery be scheduled, and what can we expect?,What therapies should we start now to support my child's development?,Are there other conditions that look similar that we should rule out?,How often should my child be seen by each specialist?,Are there any research studies or registries we can participate in?

Common questions about Dysmorphism-cleft palate-loose skin syndrome

What is Dysmorphism-cleft palate-loose skin syndrome?

Dysmorphism-cleft palate-loose skin syndrome is an extremely rare genetic condition that affects multiple parts of the body. It is sometimes referred to by its Orphanet designation (ORPHA:1779). The syndrome is characterized by a combination of unusual facial features (dysmorphism), an opening in the roof of the mouth (cleft palate), and abnormally loose or stretchy skin. Children born with this condition may also have growth delays, intellectual disability, and skeletal abnormalities. The loose skin can resemble conditions like cutis laxa, where the skin hangs in folds and lacks normal elasti

How is Dysmorphism-cleft palate-loose skin syndrome inherited?

Dysmorphism-cleft palate-loose skin syndrome follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Dysmorphism-cleft palate-loose skin syndrome typically begin?

Typical onset of Dysmorphism-cleft palate-loose skin syndrome is neonatal. Age of onset can vary across affected individuals.