DNAJB2-related Charcot-Marie-Tooth disease type 2

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ORPHA:443950OMIM:614881G60.0
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8Treatment centers

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Overview

DNAJB2-related Charcot-Marie-Tooth disease type 2 (also called CMT2 caused by DNAJB2 mutations, or sometimes referred to as DNAJB2-CMT) is a rare inherited nerve disease that affects the peripheral nervous system — the network of nerves outside the brain and spinal cord. These nerves carry signals between the brain and the muscles and skin, especially in the arms and legs. When the DNAJB2 gene does not work properly, nerve fibers gradually break down over time, leading to muscle weakness and loss of sensation. The most common symptoms include weakness and wasting of the muscles in the feet, lower legs, hands, and forearms. People often notice difficulty walking, foot deformities such as high arches or hammertoes, and reduced ability to feel touch, pain, or temperature in the hands and feet. Balance problems are also common. Symptoms usually begin in childhood, adolescence, or early adulthood and slowly get worse over many years. There is currently no cure for DNAJB2-related CMT2. Treatment focuses on managing symptoms and maintaining quality of life. Physical therapy, occupational therapy, orthotic devices such as ankle-foot braces, and pain management are the main tools available. A team of specialists works together to help people stay as active and independent as possible. While the disease is slowly progressive, most people have a normal or near-normal lifespan.

Also known as:

Key symptoms:

Muscle weakness in the feet and lower legsMuscle weakness in the hands and forearmsMuscle wasting (shrinking) in the lower legs and feetHigh foot arches (pes cavus)Hammertoes or other foot deformitiesDifficulty walking or frequent trippingReduced or absent reflexes, especially at the anklesNumbness or reduced sensation in the feet and handsDifficulty feeling temperature or pain in the extremitiesBalance problems and unsteady gaitFatigue with physical activityDifficulty with fine hand movements such as buttoning clothes

Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for DNAJB2-related Charcot-Marie-Tooth disease type 2.

View clinical trials →

No actively recruiting trials found for DNAJB2-related Charcot-Marie-Tooth disease type 2 at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the DNAJB2-related Charcot-Marie-Tooth disease type 2 community →

No specialists are currently listed for DNAJB2-related Charcot-Marie-Tooth disease type 2.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to DNAJB2-related Charcot-Marie-Tooth disease type 2.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about DNAJB2-related Charcot-Marie-Tooth disease type 2

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific change was found in my DNAJB2 gene, and what does it mean for my health?,How quickly is my condition likely to progress, and what signs should I watch for?,Should other family members be tested for this gene change?,What therapies or devices would help me most right now?,Are there any clinical trials I might be eligible for?,What specialists should be part of my care team, and how often should I be seen?,Are there any activities or medications I should avoid because of my condition?

Common questions about DNAJB2-related Charcot-Marie-Tooth disease type 2

What is DNAJB2-related Charcot-Marie-Tooth disease type 2?

DNAJB2-related Charcot-Marie-Tooth disease type 2 (also called CMT2 caused by DNAJB2 mutations, or sometimes referred to as DNAJB2-CMT) is a rare inherited nerve disease that affects the peripheral nervous system — the network of nerves outside the brain and spinal cord. These nerves carry signals between the brain and the muscles and skin, especially in the arms and legs. When the DNAJB2 gene does not work properly, nerve fibers gradually break down over time, leading to muscle weakness and loss of sensation. The most common symptoms include weakness and wasting of the muscles in the feet, l

How is DNAJB2-related Charcot-Marie-Tooth disease type 2 inherited?

DNAJB2-related Charcot-Marie-Tooth disease type 2 follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.