Distal triplication 15q syndrome

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ORPHA:314588OMIM:614846Q99.8
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Overview

Distal triplication 15q syndrome is a very rare chromosomal disorder in which a segment of the long arm (q arm) of chromosome 15, specifically the distal (far end) portion, is present in three copies instead of the usual two. This extra genetic material disrupts normal development and leads to a range of physical and developmental problems. The condition is sometimes referred to as trisomy of the distal 15q region or distal 15q triplication. People with this syndrome typically experience intellectual disability, developmental delays, distinctive facial features, and growth problems. Some individuals may also have heart defects, skeletal abnormalities, and seizures. The severity of symptoms can vary depending on the exact size and location of the triplicated segment. Larger triplications tend to cause more significant health issues. There is currently no cure for distal triplication 15q syndrome. Treatment focuses on managing individual symptoms and supporting development. This may include early intervention therapies such as speech therapy, physical therapy, and occupational therapy. Heart defects or other structural problems may require surgical correction. Regular monitoring by a team of specialists is important to address the various health concerns that can arise throughout life.

Also known as:

Key symptoms:

Intellectual disabilityDevelopmental delaysUnusual facial featuresGrowth delays or short statureLow muscle tone (floppiness)Seizures or epilepsyHeart defects present at birthFeeding difficulties in infancySpeech and language delaysSkeletal abnormalitiesSmall head sizeBehavioral difficultiesVision problemsHearing problemsDelayed motor milestones such as sitting and walking

Clinical phenotype terms (45)— hover any for plain English
Growth abnormalityHP:0001507Birth length greater than 97th percentileHP:0003517Hydrocele testisHP:0000034Polycystic kidney dysplasiaHP:0000113
Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Distal triplication 15q syndrome.

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No actively recruiting trials found for Distal triplication 15q syndrome at this time.

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No specialists are currently listed for Distal triplication 15q syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Distal triplication 15q syndrome.

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Community

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Latest news about Distal triplication 15q syndrome

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Caregiver Resources

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Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is the exact size and location of the triplication on chromosome 15, and how does that affect my child's prognosis?,Should other family members be tested for chromosomal rearrangements?,What early intervention therapies do you recommend, and how soon should they start?,Are there any heart defects or other organ problems that need to be monitored?,What is the risk of seizures, and what should I do if one occurs?,What educational supports and services should I look into for my child?,Are there any research studies or registries we should consider joining?

Common questions about Distal triplication 15q syndrome

What is Distal triplication 15q syndrome?

Distal triplication 15q syndrome is a very rare chromosomal disorder in which a segment of the long arm (q arm) of chromosome 15, specifically the distal (far end) portion, is present in three copies instead of the usual two. This extra genetic material disrupts normal development and leads to a range of physical and developmental problems. The condition is sometimes referred to as trisomy of the distal 15q region or distal 15q triplication. People with this syndrome typically experience intellectual disability, developmental delays, distinctive facial features, and growth problems. Some indi

At what age does Distal triplication 15q syndrome typically begin?

Typical onset of Distal triplication 15q syndrome is neonatal. Age of onset can vary across affected individuals.