Disorder of tryptophan metabolism

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ORPHA:289829
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7Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Disorder of tryptophan metabolism is a rare group of inherited metabolic conditions in which the body cannot properly break down or use tryptophan, an essential amino acid found in many protein-rich foods. Tryptophan is important because the body uses it to make serotonin (a brain chemical that affects mood and sleep), niacin (vitamin B3), and other vital substances. When the enzymes responsible for processing tryptophan do not work correctly, harmful byproducts can build up in the body, or the body may not produce enough of the important chemicals it needs. Symptoms can vary widely depending on which specific step in the tryptophan pathway is affected. Some patients may experience skin rashes, sensitivity to sunlight, developmental delays, intellectual disability, problems with coordination, or psychiatric symptoms such as mood changes. In some forms, patients may develop pellagra-like symptoms due to niacin deficiency, including skin inflammation, diarrhea, and confusion. Hartnup disease is one of the better-known conditions in this group, where tryptophan and other amino acids are not properly absorbed in the gut and kidneys. Treatment is generally supportive and depends on the specific type of tryptophan metabolism disorder. It may include dietary modifications, niacin or nicotinamide supplementation, sun protection, and management of neurological or psychiatric symptoms. Early diagnosis and ongoing metabolic management can help improve quality of life and prevent complications.

Key symptoms:

Skin rash, especially after sun exposureSensitivity to sunlightRed, scaly skin similar to pellagraDiarrhea or loose stoolsIntellectual disability or learning difficultiesDevelopmental delays in childrenPoor coordination or unsteady walkingMood changes or emotional instabilityConfusion or difficulty thinking clearlyShort stature or poor growthSeizures in some casesFatigue or low energyUnusual urine odor or color

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

FDA & Trial Timeline

3 events
Sep 2026Impact of Humid-Heat on Gut-Tryptophan-Stone Pathway

Shanghai General Hospital, Shanghai Jiao Tong University School of Medicine

TrialNOT YET RECRUITING
Feb 2024Tryptophan-Kynurenine Pathway Metabolism in the Pathophysiology of Cognitive Impairment in Schizophrenia.

Tianjin Anding Hospital

TrialENROLLING BY INVITATION
Dec 2022Tryptophan for Impaired AhR Signaling in Celiac Disease

McMaster University — NA

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Disorder of tryptophan metabolism.

View clinical trials →

No actively recruiting trials found for Disorder of tryptophan metabolism at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Disorder of tryptophan metabolism community →

Specialists

7 foundView all specialists →
MP
Marta Ramón Krauel, PI
Specialist
PI on 1 active trial7 Disorder of tryptophan metabolism publications
MK
Marjukka Kolehmainen
Specialist
PI on 2 active trials
AP
Ali Ünlü, Professor
Specialist
PI on 1 active trial1 Disorder of tryptophan metabolism publication
MP
Marielle P Engelen, PhD
Specialist
PI on 1 active trial
OM
Oliver Freudenreich, M.D.
BOSTON, MA
Specialist
PI on 1 active trial
PP
Petra Reinke, Md PhD
Specialist
PI on 1 active trial
AM
Alfred Königsrainer, Prof., M.D.
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Disorder of tryptophan metabolism.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Disorder of tryptophan metabolism

Disease timeline:

New recruiting trial: Tryptophan for Impaired AhR Signaling in Celiac Disease

A new clinical trial is recruiting patients for Disorder of tryptophan metabolism

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific type of tryptophan metabolism disorder does my child or I have?,Which gene is affected, and what does that mean for our family?,What supplements or vitamins should be taken, and at what doses?,Are there specific foods to eat more of or avoid?,How much sun exposure is safe, and what precautions should we take?,Will this condition affect brain development or learning ability?,How often should we have follow-up appointments and lab tests?

Common questions about Disorder of tryptophan metabolism

What is Disorder of tryptophan metabolism?

Disorder of tryptophan metabolism is a rare group of inherited metabolic conditions in which the body cannot properly break down or use tryptophan, an essential amino acid found in many protein-rich foods. Tryptophan is important because the body uses it to make serotonin (a brain chemical that affects mood and sleep), niacin (vitamin B3), and other vital substances. When the enzymes responsible for processing tryptophan do not work correctly, harmful byproducts can build up in the body, or the body may not produce enough of the important chemicals it needs. Symptoms can vary widely depending

Which specialists treat Disorder of tryptophan metabolism?

7 specialists and care centers treating Disorder of tryptophan metabolism are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.