Disorder of phospholipids, sphingolipids and fatty acids biosynthesis with peripheral nerves predominant involvement

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:352309
Who is this for?
Show terms as
8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Disorder of phospholipids, sphingolipids, and fatty acids biosynthesis with peripheral nerves predominant involvement is a group of rare inherited metabolic conditions that affect how the body makes certain types of fats (lipids). These lipids — including phospholipids, sphingolipids, and fatty acids — are essential building blocks of nerve cell membranes, particularly the myelin sheath that insulates peripheral nerves (the nerves outside the brain and spinal cord). When the body cannot properly produce these lipids, the peripheral nerves become damaged or do not function correctly, leading to a condition similar to peripheral neuropathy. Patients typically experience numbness, tingling, weakness, and pain in the hands and feet that can gradually spread. Some individuals may also have difficulty with balance and coordination. The severity and age of onset can vary depending on the specific genetic cause. Because these disorders affect lipid metabolism at a fundamental level, the symptoms tend to be progressive, meaning they may worsen over time. Currently, there are no curative treatments for most conditions in this group. Management focuses on symptom relief, physical therapy to maintain mobility and strength, pain management, and supportive care. Research is ongoing to better understand the underlying mechanisms and develop targeted therapies. Early diagnosis through genetic testing is important to guide management and provide families with accurate genetic counseling.

Key symptoms:

Numbness or tingling in hands and feetMuscle weakness in the arms and legsBurning or shooting nerve painDifficulty walking or balance problemsLoss of sensation in the extremitiesMuscle wasting, especially in the lower legsReduced reflexesFoot deformities such as high arches or hammertoesDifficulty with fine motor tasks like buttoning clothesFatigueSensitivity to cold temperaturesCramping in the legs or feet

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Disorder of phospholipids, sphingolipids and fatty acids biosynthesis with peripheral nerves predominant involvement.

View clinical trials →

No actively recruiting trials found for Disorder of phospholipids, sphingolipids and fatty acids biosynthesis with peripheral nerves predominant involvement at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Disorder of phospholipids, sphingolipids and fatty acids biosynthesis with peripheral nerves predominant involvement community →

No specialists are currently listed for Disorder of phospholipids, sphingolipids and fatty acids biosynthesis with peripheral nerves predominant involvement.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Disorder of phospholipids, sphingolipids and fatty acids biosynthesis with peripheral nerves predominant involvement.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Disorder of phospholipids, sphingolipids and fatty acids biosynthesis with peripheral nerves predominant involvementForum →

No community posts yet. Be the first to share your experience with Disorder of phospholipids, sphingolipids and fatty acids biosynthesis with peripheral nerves predominant involvement.

Start the conversation →

Latest news about Disorder of phospholipids, sphingolipids and fatty acids biosynthesis with peripheral nerves predominant involvement

No recent news articles for Disorder of phospholipids, sphingolipids and fatty acids biosynthesis with peripheral nerves predominant involvement.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific type of lipid biosynthesis disorder do I have, and which gene is affected?,How quickly is this condition likely to progress in my case?,What therapies or treatments can help manage my symptoms right now?,Should my family members be tested for this condition?,Are there any clinical trials or experimental treatments I might be eligible for?,What specialists should I see regularly, and how often?,What can I do at home to slow down the progression or maintain my function?

Common questions about Disorder of phospholipids, sphingolipids and fatty acids biosynthesis with peripheral nerves predominant involvement

What is Disorder of phospholipids, sphingolipids and fatty acids biosynthesis with peripheral nerves predominant involvement?

Disorder of phospholipids, sphingolipids, and fatty acids biosynthesis with peripheral nerves predominant involvement is a group of rare inherited metabolic conditions that affect how the body makes certain types of fats (lipids). These lipids — including phospholipids, sphingolipids, and fatty acids — are essential building blocks of nerve cell membranes, particularly the myelin sheath that insulates peripheral nerves (the nerves outside the brain and spinal cord). When the body cannot properly produce these lipids, the peripheral nerves become damaged or do not function correctly, leading to