Dianzani autoimmune lymphoproliferative disease

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:275523OMIM:605233D47.9
Who is this for?
Show terms as
8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Dianzani autoimmune lymphoproliferative disease (also known as DALD or Dianzani autoimmune lymphoproliferative syndrome) is a rare condition that affects the immune system. In this disease, the body's immune system does not properly regulate itself, leading to an overgrowth (proliferation) of certain white blood cells called lymphocytes. Normally, the body has a built-in process called apoptosis (programmed cell death) that removes immune cells when they are no longer needed. In DALD, this process does not work correctly, so excess lymphocytes build up and can cause problems throughout the body. People with DALD may experience enlarged lymph nodes, an enlarged spleen, and autoimmune problems where the immune system mistakenly attacks the body's own healthy cells. This can lead to low blood counts, including anemia (low red blood cells), low platelet counts (which can cause easy bruising and bleeding), and low white blood cell counts (which can increase infection risk). The condition shares features with the better-known autoimmune lymphoproliferative syndrome (ALPS) but is considered a distinct entity because it involves different underlying genetic mechanisms. Treatment for DALD is mainly focused on managing symptoms and controlling the overactive immune system. Doctors may use immunosuppressive medications to calm the immune response. Regular monitoring by specialists is important to watch for complications, including a slightly increased risk of lymphoma (a type of blood cancer). Early diagnosis and ongoing care can help improve quality of life for people living with this condition.

Also known as:

Key symptoms:

Enlarged lymph nodes (swollen glands)Enlarged spleenEnlarged liverAnemia (low red blood cells causing tiredness and paleness)Low platelet count (easy bruising or bleeding)Low white blood cell count (frequent infections)Autoimmune destruction of red blood cellsAutoimmune destruction of plateletsFatigue and low energyRecurrent infectionsUnexplained feversSkin rashes related to autoimmune activity

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Childhood

Begins in childhood, roughly ages 1 to 12

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Dianzani autoimmune lymphoproliferative disease.

View clinical trials →

No actively recruiting trials found for Dianzani autoimmune lymphoproliferative disease at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Dianzani autoimmune lymphoproliferative disease community →

No specialists are currently listed for Dianzani autoimmune lymphoproliferative disease.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Dianzani autoimmune lymphoproliferative disease.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Dianzani autoimmune lymphoproliferative diseaseForum →

No community posts yet. Be the first to share your experience with Dianzani autoimmune lymphoproliferative disease.

Start the conversation →

Latest news about Dianzani autoimmune lymphoproliferative disease

No recent news articles for Dianzani autoimmune lymphoproliferative disease.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific genetic change is causing my (or my child's) condition?,How often will blood counts need to be monitored?,What are the signs that the disease is getting worse and when should I seek emergency care?,What medications are recommended, and what are their side effects?,What is the long-term risk of developing lymphoma, and how will you screen for it?,Are there any activities or medications my child should avoid?,Should other family members be tested for this condition?

Common questions about Dianzani autoimmune lymphoproliferative disease

What is Dianzani autoimmune lymphoproliferative disease?

Dianzani autoimmune lymphoproliferative disease (also known as DALD or Dianzani autoimmune lymphoproliferative syndrome) is a rare condition that affects the immune system. In this disease, the body's immune system does not properly regulate itself, leading to an overgrowth (proliferation) of certain white blood cells called lymphocytes. Normally, the body has a built-in process called apoptosis (programmed cell death) that removes immune cells when they are no longer needed. In DALD, this process does not work correctly, so excess lymphocytes build up and can cause problems throughout the bod

At what age does Dianzani autoimmune lymphoproliferative disease typically begin?

Typical onset of Dianzani autoimmune lymphoproliferative disease is childhood. Age of onset can vary across affected individuals.