Deep dermatophytosis

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Overview

Deep dermatophytosis, also called invasive dermatophytosis or deep dermatophyte infection, is a rare and serious fungal infection where common skin fungi (dermatophytes) invade beyond the skin surface into deeper tissues such as the lymph nodes, brain, and other internal organs. Normally, dermatophytes only cause superficial infections like athlete's foot or ringworm. However, in people with certain inherited immune system defects, these fungi can penetrate deep into the body and cause life-threatening disease. The condition typically affects people who have genetic mutations that weaken a specific part of their immune defense against fungi. Patients may first notice persistent or widespread skin infections that do not respond to standard antifungal treatments. Over time, the infection can spread to the lymph nodes, bones, and even the brain. Skin lesions may appear as deep nodules, abscesses, or large crusty plaques that keep growing despite treatment. Treatment involves long-term antifungal medications, often given by mouth or through an IV. Drugs such as terbinafine, itraconazole, voriconazole, and posaconazole are commonly used. Despite treatment, the infection can be very difficult to control, and relapses are common. In some cases, the disease can be fatal, especially when it spreads to the brain or other vital organs. Early diagnosis and aggressive treatment are essential to improve outcomes.

Also known as:

Key symptoms:

Widespread or severe skin fungal infections that won't healDeep skin nodules or lumpsSkin abscesses or boils caused by fungal infectionThick, crusty skin plaquesSwollen lymph nodesFungal infection spreading to lymph nodesFungal infection of the brain (rare but serious)Recurrent ringworm-like rashes that keep coming backSevere nail fungal infectionsScalp infections with hair lossFever and general feeling of being unwellWeight lossScarring of the skin from chronic infections

Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Deep dermatophytosis.

View clinical trials →

No actively recruiting trials found for Deep dermatophytosis at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Deep dermatophytosis community →

No specialists are currently listed for Deep dermatophytosis.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Deep dermatophytosis.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Deep dermatophytosis

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific genetic mutation is causing my immune system to be vulnerable to this infection?,How far has the fungal infection spread, and what tests do I need to check for deep organ involvement?,What antifungal medications will I need, and how long will I need to take them?,What side effects should I watch for with long-term antifungal treatment?,Is bone marrow transplant an option for me or my child?,Should my family members be tested for the same genetic mutation?,Are there any clinical trials or new treatments being studied for this condition?

Common questions about Deep dermatophytosis

What is Deep dermatophytosis?

Deep dermatophytosis, also called invasive dermatophytosis or deep dermatophyte infection, is a rare and serious fungal infection where common skin fungi (dermatophytes) invade beyond the skin surface into deeper tissues such as the lymph nodes, brain, and other internal organs. Normally, dermatophytes only cause superficial infections like athlete's foot or ringworm. However, in people with certain inherited immune system defects, these fungi can penetrate deep into the body and cause life-threatening disease. The condition typically affects people who have genetic mutations that weaken a sp

How is Deep dermatophytosis inherited?

Deep dermatophytosis follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.