Cystic hamartoma of lung and kidney

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Overview

Cystic hamartoma of lung and kidney is an extremely rare condition in which abnormal, non-cancerous growths called hamartomas develop in both the lungs and the kidneys. These hamartomas are made up of a disorganized mix of tissues that are normally found in these organs, but they grow in a cyst-like (fluid-filled sac) pattern. The condition is typically identified in newborns or very young infants and may be detected before birth on prenatal ultrasound. Affected babies may have breathing difficulties due to the lung cysts and kidney problems due to the renal cysts. The lung involvement can range from mild to severe, and in some cases the cysts can be large enough to compress surrounding lung tissue, leading to respiratory distress. The kidney cysts can impair normal kidney function. Because this condition is so rare, with only a handful of cases reported in the medical literature, there is no established standard treatment. Management is supportive and depends on the severity of symptoms. Surgical removal of problematic cysts may be considered, and respiratory support may be needed for infants with significant lung involvement. Kidney function is monitored closely. The long-term outlook varies depending on how severely the lungs and kidneys are affected.

Also known as:

Key symptoms:

Cysts in the lungsCysts in the kidneysBreathing difficulties in newbornsRapid breathingLow oxygen levelsEnlarged kidneysReduced kidney functionAbdominal swellingFailure to thrive or poor weight gainRespiratory distress at birth

Clinical phenotype terms (5)— hover any for plain English
Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Cystic hamartoma of lung and kidney.

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No actively recruiting trials found for Cystic hamartoma of lung and kidney at this time.

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No specialists are currently listed for Cystic hamartoma of lung and kidney.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Cystic hamartoma of lung and kidney.

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Community

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.How severe are the cysts in my child's lungs and kidneys?,Will my child need surgery to remove any of the cysts?,What kind of respiratory support might be needed?,How will kidney function be monitored over time?,Is genetic testing recommended to rule out other conditions?,What is the expected long-term outlook for my child?,Are there any specialists or centers with experience treating this condition?

Common questions about Cystic hamartoma of lung and kidney

What is Cystic hamartoma of lung and kidney?

Cystic hamartoma of lung and kidney is an extremely rare condition in which abnormal, non-cancerous growths called hamartomas develop in both the lungs and the kidneys. These hamartomas are made up of a disorganized mix of tissues that are normally found in these organs, but they grow in a cyst-like (fluid-filled sac) pattern. The condition is typically identified in newborns or very young infants and may be detected before birth on prenatal ultrasound. Affected babies may have breathing difficulties due to the lung cysts and kidney problems due to the renal cysts. The lung involvement can ran

At what age does Cystic hamartoma of lung and kidney typically begin?

Typical onset of Cystic hamartoma of lung and kidney is neonatal. Age of onset can vary across affected individuals.