Cystadenoma of childhood

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ORPHA:206470D27
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Overview

Cystadenoma of childhood (Orphanet code 206470) is a rare benign ovarian tumor occurring in pediatric patients. As indicated by the ICD-10 code D27 (benign neoplasm of ovary), this condition involves the development of cystic, fluid-filled tumors within the ovary. Ovarian cystadenomas in childhood are uncommon, as these tumors are far more frequently encountered in adult women. They can be classified as serous or mucinous subtypes based on the type of epithelial lining and fluid content. The reproductive system is the primary body system affected. Clinically, children with ovarian cystadenomas may present with abdominal pain, abdominal distension or swelling, and a palpable abdominal or pelvic mass. In some cases, the tumor may be discovered incidentally during imaging for other reasons. Complications can include ovarian torsion, which may present as acute abdominal pain requiring emergency intervention. Hormonal disturbances are generally not a feature of these tumors, as cystadenomas are typically non-functional. Diagnosis is usually established through imaging studies such as ultrasound and confirmed by histopathological examination after surgical removal. The primary treatment is surgical excision, with ovary-sparing surgery (cystectomy) being the preferred approach in pediatric patients to preserve future fertility. The prognosis is generally excellent, as these tumors are benign with a very low risk of recurrence after complete surgical removal. Malignant transformation is exceedingly rare in the pediatric population.

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Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Childhood

Begins in childhood, roughly ages 1 to 12

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Cystadenoma of childhood.

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No actively recruiting trials found for Cystadenoma of childhood at this time.

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No specialists are currently listed for Cystadenoma of childhood.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Cystadenoma of childhood.

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Community

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Common questions about Cystadenoma of childhood

What is Cystadenoma of childhood?

Cystadenoma of childhood (Orphanet code 206470) is a rare benign ovarian tumor occurring in pediatric patients. As indicated by the ICD-10 code D27 (benign neoplasm of ovary), this condition involves the development of cystic, fluid-filled tumors within the ovary. Ovarian cystadenomas in childhood are uncommon, as these tumors are far more frequently encountered in adult women. They can be classified as serous or mucinous subtypes based on the type of epithelial lining and fluid content. The reproductive system is the primary body system affected. Clinically, children with ovarian cystadenoma

How is Cystadenoma of childhood inherited?

Cystadenoma of childhood follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Cystadenoma of childhood typically begin?

Typical onset of Cystadenoma of childhood is childhood. Age of onset can vary across affected individuals.