Cryptomicrotia-brachydactyly-excess fingertip arch syndrome

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:1547OMIM:123560Q87.8
Who is this for?
Show terms as
8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Cryptomicrotia-brachydactyly-excess fingertip arch syndrome is an extremely rare genetic condition that affects the development of the ears, hands, and fingerprint patterns. The name describes its three main features: cryptomicrotia (unusually small ears that may be partially hidden under the skin), brachydactyly (abnormally short fingers and/or toes), and an excess of arch-type fingerprint patterns (most people have a mix of loops, whorls, and arches, but individuals with this syndrome have an unusually high number of arches on their fingertips). This condition is present from birth and is classified under congenital malformation syndromes. Because the syndrome is so rare, with very few cases described in the medical literature, our understanding of the full range of symptoms and the best approaches to management is limited. There is no specific cure for this condition. Treatment is supportive and focuses on addressing individual symptoms. For example, if the small ears affect hearing, hearing aids or surgical options may be considered. Hand function may be evaluated and supported through occupational therapy if short fingers cause difficulty with fine motor tasks. Genetic counseling is recommended for affected families to understand the inheritance pattern and recurrence risk. Patients benefit from a team of specialists who can address the different body systems involved.

Also known as:

Key symptoms:

Unusually small ears (microtia)Ears partially buried or hidden under the skin (cryptotia)Short fingers (brachydactyly)Short toesExcess arch patterns on fingertipsPossible mild hearing difficultiesUnusual ear shape or positioningPossible difficulty with fine motor tasks due to short fingers

Clinical phenotype terms (7)— hover any for plain English
BrachytelomesophalangyHP:0005872
Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Cryptomicrotia-brachydactyly-excess fingertip arch syndrome.

View clinical trials →

No actively recruiting trials found for Cryptomicrotia-brachydactyly-excess fingertip arch syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Cryptomicrotia-brachydactyly-excess fingertip arch syndrome community →

No specialists are currently listed for Cryptomicrotia-brachydactyly-excess fingertip arch syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Cryptomicrotia-brachydactyly-excess fingertip arch syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Cryptomicrotia-brachydactyly-excess fingertip arch syndromeForum →

No community posts yet. Be the first to share your experience with Cryptomicrotia-brachydactyly-excess fingertip arch syndrome.

Start the conversation →

Latest news about Cryptomicrotia-brachydactyly-excess fingertip arch syndrome

No recent news articles for Cryptomicrotia-brachydactyly-excess fingertip arch syndrome.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Does my child have any hearing loss related to the ear abnormalities, and should we schedule regular hearing tests?,Are there surgical options to improve the appearance or function of the ears?,Would occupational therapy help improve hand function and fine motor skills?,Is genetic testing available to identify the cause, and what would the results mean for our family?,What is the chance that future children could also have this condition?,Are there any other health problems we should watch for as my child grows?,Can you connect us with other families or support groups for rare craniofacial or limb conditions?

Common questions about Cryptomicrotia-brachydactyly-excess fingertip arch syndrome

What is Cryptomicrotia-brachydactyly-excess fingertip arch syndrome?

Cryptomicrotia-brachydactyly-excess fingertip arch syndrome is an extremely rare genetic condition that affects the development of the ears, hands, and fingerprint patterns. The name describes its three main features: cryptomicrotia (unusually small ears that may be partially hidden under the skin), brachydactyly (abnormally short fingers and/or toes), and an excess of arch-type fingerprint patterns (most people have a mix of loops, whorls, and arches, but individuals with this syndrome have an unusually high number of arches on their fingertips). This condition is present from birth and is cl

How is Cryptomicrotia-brachydactyly-excess fingertip arch syndrome inherited?

Cryptomicrotia-brachydactyly-excess fingertip arch syndrome follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Cryptomicrotia-brachydactyly-excess fingertip arch syndrome typically begin?

Typical onset of Cryptomicrotia-brachydactyly-excess fingertip arch syndrome is neonatal. Age of onset can vary across affected individuals.