Congenital pseudoarthrosis of the fibula

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Overview

Congenital pseudoarthrosis of the fibula is a very rare bone condition that is present at birth. The fibula is the thinner bone on the outer side of the lower leg, running alongside the larger shinbone (tibia). In this condition, the fibula fails to form properly and develops a "false joint" (pseudoarthrosis), meaning there is an abnormal gap or area of non-union in the bone where it should be continuous and solid. This can lead to instability of the ankle, deformity of the lower leg, and difficulty with walking and weight-bearing activities. Children with this condition may be noticed to have a bowing or angulation of the lower leg, ankle instability, or a limp. The condition can sometimes be associated with neurofibromatosis type 1 (NF1), a genetic disorder that affects how nerve tissue grows. However, congenital pseudoarthrosis of the fibula can also occur on its own without any associated syndrome. Treatment is primarily surgical and aims to stabilize the ankle joint and correct any deformity. Options may include bone grafting, internal fixation with plates or rods, and in some cases bracing. The condition is much rarer than congenital pseudoarthrosis of the tibia, and management often requires a team of specialists experienced in complex pediatric orthopedic problems. Early diagnosis and treatment are important to prevent progressive deformity and to support normal walking development.

Also known as:

Key symptoms:

Bowing or angulation of the lower legAnkle instability or loosenessLimping or abnormal walking patternPain in the lower leg or ankle areaShortening of the affected legDifficulty bearing weight on the affected legVisible deformity of the lower legSwelling near the ankleReduced range of motion at the ankleFrequent ankle sprains or giving way

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Congenital pseudoarthrosis of the fibula.

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No actively recruiting trials found for Congenital pseudoarthrosis of the fibula at this time.

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No specialists are currently listed for Congenital pseudoarthrosis of the fibula.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Congenital pseudoarthrosis of the fibula.

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Community

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Caregiver Resources

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Questions for your doctor

Bring these to your next appointment

  • Q1.Is my child's condition associated with neurofibromatosis type 1, and should we do genetic testing?,What surgical options are available, and what are the risks and expected outcomes?,Will my child need more than one surgery over time?,What kind of bracing or physical therapy will be needed?,How will this condition affect my child's growth and leg length as they get older?,Are there any activities my child should avoid?,What signs should I watch for that would mean we need to come back sooner than planned?

Common questions about Congenital pseudoarthrosis of the fibula

What is Congenital pseudoarthrosis of the fibula?

Congenital pseudoarthrosis of the fibula is a very rare bone condition that is present at birth. The fibula is the thinner bone on the outer side of the lower leg, running alongside the larger shinbone (tibia). In this condition, the fibula fails to form properly and develops a "false joint" (pseudoarthrosis), meaning there is an abnormal gap or area of non-union in the bone where it should be continuous and solid. This can lead to instability of the ankle, deformity of the lower leg, and difficulty with walking and weight-bearing activities. Children with this condition may be noticed to hav

At what age does Congenital pseudoarthrosis of the fibula typically begin?

Typical onset of Congenital pseudoarthrosis of the fibula is neonatal. Age of onset can vary across affected individuals.