Congenital muscular dystrophy without intellectual disability

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ORPHA:370980OMIM:606612G71.2
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Overview

Congenital muscular dystrophy without intellectual disability (CMD without intellectual disability) is a group of rare inherited muscle disorders that are present from birth or early infancy. Unlike some other forms of congenital muscular dystrophy, this type does not affect thinking, learning, or brain development. The main feature is muscle weakness that is noticeable from a very young age. Babies may appear floppy (a condition called hypotonia), have difficulty feeding, and may be slow to reach movement milestones like sitting up, crawling, or walking. The disease affects the skeletal muscles — the muscles used for movement. Over time, some children may develop joint stiffness (contractures) and curvature of the spine (scoliosis). The severity varies widely: some individuals can walk independently while others may need a wheelchair. Breathing muscles can also be affected, sometimes requiring respiratory support, especially during sleep or illness. There is currently no cure for congenital muscular dystrophy without intellectual disability. Treatment focuses on managing symptoms and maintaining quality of life. This includes physical therapy to preserve mobility and prevent contractures, orthopedic interventions for spine and joint problems, and respiratory support when needed. A team of specialists typically works together to provide comprehensive care. Early diagnosis and proactive management can significantly improve outcomes and help affected individuals live fuller lives.

Also known as:

Key symptoms:

Muscle weakness present from birth or early infancyFloppy baby (low muscle tone)Delayed motor milestones like sitting and walkingJoint stiffness or contracturesCurvature of the spine (scoliosis)Difficulty feeding in infancyBreathing difficulties, especially during sleepElevated creatine kinase levels in bloodDifficulty with fine motor tasksMuscle wasting over timeFatigue with physical activityRigid spine in some subtypesSkin changes in some subtypes (such as Ullrich CMD)

Clinical phenotype terms (27)— hover any for plain English
Facial diplegiaHP:0001349Achilles tendon contractureHP:0001771Limb-girdle muscle atrophyHP:0003797Proximal amyotrophyHP:0007126Fatty replacement of skeletal muscleHP:0012548Reduced muscle fiber alpha dystroglycanHP:0030099
Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Congenital muscular dystrophy without intellectual disability.

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No actively recruiting trials found for Congenital muscular dystrophy without intellectual disability at this time.

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No specialists are currently listed for Congenital muscular dystrophy without intellectual disability.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Congenital muscular dystrophy without intellectual disability.

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Community

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Caregiver Resources

NORD Caregiver Resources

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Mental Health Support

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Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific genetic subtype of congenital muscular dystrophy does my child have, and what does that mean for their future?,How often should we have respiratory function tested, and what signs of breathing problems should we watch for?,What physical therapy program is recommended, and how often should sessions occur?,Are there any clinical trials or emerging treatments that might be relevant for our specific subtype?,What school accommodations should we request to support my child's learning and participation?,Should other family members be tested for this genetic condition?,What is the recommended schedule for follow-up visits with each specialist on the care team?

Common questions about Congenital muscular dystrophy without intellectual disability

What is Congenital muscular dystrophy without intellectual disability?

Congenital muscular dystrophy without intellectual disability (CMD without intellectual disability) is a group of rare inherited muscle disorders that are present from birth or early infancy. Unlike some other forms of congenital muscular dystrophy, this type does not affect thinking, learning, or brain development. The main feature is muscle weakness that is noticeable from a very young age. Babies may appear floppy (a condition called hypotonia), have difficulty feeding, and may be slow to reach movement milestones like sitting up, crawling, or walking. The disease affects the skeletal musc

At what age does Congenital muscular dystrophy without intellectual disability typically begin?

Typical onset of Congenital muscular dystrophy without intellectual disability is neonatal. Age of onset can vary across affected individuals.