Cleft palate-short stature-vertebral anomalies syndrome

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:2015Q87.0
Who is this for?
Show terms as
8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Cleft palate-short stature-vertebral anomalies syndrome is an extremely rare genetic condition that affects several parts of the body at the same time. The three main features are a cleft palate (an opening in the roof of the mouth), short stature (being significantly shorter than expected for age), and abnormalities of the bones in the spine (vertebral anomalies). Children born with this condition may also have other skeletal problems and distinctive facial features. The cleft palate can cause difficulties with feeding in infancy, speech development, and may lead to frequent ear infections. Short stature becomes more apparent as the child grows, and the vertebral anomalies can vary in severity, sometimes leading to scoliosis (curvature of the spine) or other spinal problems. Some affected individuals may also have mild intellectual differences, though this is not always the case. Because this syndrome is so rare, there is no single cure. Treatment focuses on managing each symptom individually. Surgical repair of the cleft palate is typically performed in infancy. Growth may be monitored by an endocrinologist, and orthopedic care may be needed for spinal issues. Speech therapy and regular hearing assessments are also important parts of care. A team of specialists working together provides the best outcomes for affected individuals.

Also known as:

Key symptoms:

Opening in the roof of the mouth (cleft palate)Short stature or growth delayAbnormally shaped bones in the spineCurvature of the spine (scoliosis)Feeding difficulties in infancySpeech problemsFrequent ear infectionsHearing lossDistinctive facial featuresDelayed motor developmentSkeletal abnormalities beyond the spine

Clinical phenotype terms (11)— hover any for plain English
Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Cleft palate-short stature-vertebral anomalies syndrome.

View clinical trials →

No actively recruiting trials found for Cleft palate-short stature-vertebral anomalies syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Cleft palate-short stature-vertebral anomalies syndrome community →

No specialists are currently listed for Cleft palate-short stature-vertebral anomalies syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Cleft palate-short stature-vertebral anomalies syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Cleft palate-short stature-vertebral anomalies syndromeForum →

No community posts yet. Be the first to share your experience with Cleft palate-short stature-vertebral anomalies syndrome.

Start the conversation →

Latest news about Cleft palate-short stature-vertebral anomalies syndrome

No recent news articles for Cleft palate-short stature-vertebral anomalies syndrome.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is the best timing for cleft palate repair surgery for my child?,Should my child be evaluated for growth hormone therapy?,How often should my child's spine be monitored with imaging?,What genetic testing would you recommend for our family?,When should speech therapy begin, and how often should it occur?,Are there any signs of complications I should watch for at home?,What is the long-term outlook for my child's growth and development?

Common questions about Cleft palate-short stature-vertebral anomalies syndrome

What is Cleft palate-short stature-vertebral anomalies syndrome?

Cleft palate-short stature-vertebral anomalies syndrome is an extremely rare genetic condition that affects several parts of the body at the same time. The three main features are a cleft palate (an opening in the roof of the mouth), short stature (being significantly shorter than expected for age), and abnormalities of the bones in the spine (vertebral anomalies). Children born with this condition may also have other skeletal problems and distinctive facial features. The cleft palate can cause difficulties with feeding in infancy, speech development, and may lead to frequent ear infections.

How is Cleft palate-short stature-vertebral anomalies syndrome inherited?

Cleft palate-short stature-vertebral anomalies syndrome follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Cleft palate-short stature-vertebral anomalies syndrome typically begin?

Typical onset of Cleft palate-short stature-vertebral anomalies syndrome is neonatal. Age of onset can vary across affected individuals.