Celiac artery compression syndrome

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2Active trials17Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Celiac artery compression syndrome, also known as median arcuate ligament syndrome (MALS) or Dunbar syndrome, is a condition where the median arcuate ligament — a band of fibrous tissue that connects the two sides of the diaphragm — presses on the celiac artery. The celiac artery is a major blood vessel that supplies blood to the stomach, liver, and spleen. When this ligament compresses the artery, it can reduce blood flow to these organs and also irritate nearby nerve fibers called the celiac plexus. The most common symptoms include upper abdominal pain (especially after eating), nausea, vomiting, and unintended weight loss. The pain is often described as a deep, burning, or cramping sensation in the upper belly. Some people also experience bloating or a feeling of fullness. Symptoms can vary widely — some people have mild discomfort while others have severe, debilitating pain that significantly affects their quality of life. This condition is considered anatomical rather than genetic, meaning it results from the way the body is structured rather than from a gene mutation. Treatment typically involves surgery to release the compressed artery. The most common procedure is called median arcuate ligament release, which can be done through open surgery or laparoscopically (using small incisions and a camera). In some cases, a stent or bypass procedure may also be needed to restore proper blood flow. Many patients experience significant improvement after surgery, though outcomes can vary.

Also known as:

Key symptoms:

Upper abdominal pain, especially after eatingNauseaVomitingUnintended weight lossBloating or feeling of fullness after mealsFear of eating due to pain (food avoidance)Abdominal crampingDiarrheaExercise-related abdominal painFatigue from poor nutritionAn abdominal bruit (a whooshing sound a doctor can hear with a stethoscope)

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

FDA & Trial Timeline

2 events
Jun 2024Intestinal Ischemia Biomarker in Patients With Chronic Mesenteric Ischemia

Oslo University Hospital

TrialRECRUITING
Apr 2023Coeliac Artery Release or Sham Operation

Medisch Spectrum Twente — NA

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Celiac artery compression syndrome.

2 clinical trialsare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

2 recruitingView all trials with filters →
N/A1 trial
Coeliac Artery Release or Sham Operation
N/A
Actively Recruiting
PI: RH Geelkerken, MD PHD (Medisch Spectrum Twente) · Sites: Enschede, Overijssel · Age: 1899 yrs
Other1 trial
Intestinal Ischemia Biomarker in Patients With Chronic Mesenteric Ischemia
Actively Recruiting
PI: Syed Sajid Hussain Kazmi, MD, PhD (Department of vascular surgery, Oslo University Ho) · Sites: Oslo, Oslo County · Age: 1899 yrs

Specialists

17 foundView all specialists →
SO
Shuhei Ohyama
Specialist
2 Celiac artery compression syndrome publications
TK
Toshiaki Kotani
Specialist
2 Celiac artery compression syndrome publications
YI
Yasushi Iijima
Specialist
2 Celiac artery compression syndrome publications
TS
Takahiro Sunami
Specialist
2 Celiac artery compression syndrome publications
SO
Shun Okuwaki
Specialist
2 Celiac artery compression syndrome publications
TS
Tsuyoshi Sakuma
Specialist
2 Celiac artery compression syndrome publications
SI
Shuhei Iwata
Specialist
2 Celiac artery compression syndrome publications
TA
Tsutomu Akazawa
Specialist
2 Celiac artery compression syndrome publications
KI
Kazuhide Inage
Specialist
2 Celiac artery compression syndrome publications
YS
Yasuhiro Shiga
Specialist
2 Celiac artery compression syndrome publications
SM
Shohei Minami
Specialist
2 Celiac artery compression syndrome publications
SO
Seiji Ohtori
Specialist
2 Celiac artery compression syndrome publications
RA
Raad A Aldahhas
Specialist
2 Celiac artery compression syndrome publications
RA
Rakan M Alotaibi
Specialist
2 Celiac artery compression syndrome publications
SA
Shahad S Albishi
Specialist
2 Celiac artery compression syndrome publications
RP
RH Geelkerken, MD PHD
Specialist
PI on 1 active trial
SP
Syed Sajid Hussain Kazmi, MD, PhD
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Celiac artery compression syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Celiac artery compression syndrome

Disease timeline:

New recruiting trial: Intestinal Ischemia Biomarker in Patients With Chronic Mesenteric Ischemia

A new clinical trial is recruiting patients for Celiac artery compression syndrome

New recruiting trial: Coeliac Artery Release or Sham Operation

A new clinical trial is recruiting patients for Celiac artery compression syndrome

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.How certain are you that my symptoms are caused by celiac artery compression and not another condition?,What imaging tests do I need to confirm the diagnosis?,Am I a good candidate for laparoscopic or robotic surgery, or would open surgery be better for me?,What is your experience with median arcuate ligament release surgery?,What are the chances my symptoms will improve after surgery?,Should I see a dietitian to address my weight loss and nutrition before surgery?,What should I do if my symptoms return or do not improve after surgery?

Common questions about Celiac artery compression syndrome

What is Celiac artery compression syndrome?

Celiac artery compression syndrome, also known as median arcuate ligament syndrome (MALS) or Dunbar syndrome, is a condition where the median arcuate ligament — a band of fibrous tissue that connects the two sides of the diaphragm — presses on the celiac artery. The celiac artery is a major blood vessel that supplies blood to the stomach, liver, and spleen. When this ligament compresses the artery, it can reduce blood flow to these organs and also irritate nearby nerve fibers called the celiac plexus. The most common symptoms include upper abdominal pain (especially after eating), nausea, vom

How is Celiac artery compression syndrome inherited?

Celiac artery compression syndrome follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

Are there clinical trials for Celiac artery compression syndrome?

Yes — 2 recruiting clinical trials are currently listed for Celiac artery compression syndrome on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.

Which specialists treat Celiac artery compression syndrome?

17 specialists and care centers treating Celiac artery compression syndrome are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.