Bilateral massive adrenal hemorrhage

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Overview

Bilateral massive adrenal hemorrhage is a rare and serious condition in which both adrenal glands — small organs that sit on top of each kidney — experience severe bleeding. The adrenal glands produce essential hormones such as cortisol (which helps your body respond to stress) and aldosterone (which helps control blood pressure and salt balance). When both glands are damaged by heavy bleeding, they can no longer make enough of these hormones, leading to a life-threatening condition called acute adrenal insufficiency or adrenal crisis. This condition can be triggered by several factors, including severe infections (especially meningococcal sepsis, known as Waterhouse-Friderichsen syndrome), blood clotting disorders, use of blood-thinning medications (anticoagulants), major surgery, trauma, or conditions that cause abnormal blood clotting such as antiphospholipid syndrome. Newborns can also be affected, particularly after a difficult birth. Symptoms come on suddenly and can include severe abdominal or flank pain, low blood pressure, shock, fever, nausea, vomiting, confusion, and extreme weakness. Without prompt treatment — primarily emergency replacement of cortisol and fluids — this condition can be fatal. Early recognition and aggressive supportive care are critical to survival. Long-term survivors typically need lifelong hormone replacement therapy to compensate for the lost adrenal function.

Also known as:

Key symptoms:

Sudden severe abdominal painPain in the sides or back (flank pain)Dangerously low blood pressureShock (cold, clammy skin, rapid heartbeat)High feverNausea and vomitingExtreme fatigue and weaknessConfusion or altered mental stateSkin rash or purplish spots (purpura), especially with infectionDizziness or faintingRapid weight lossLow blood sugarDehydrationDark skin discoloration (if chronic adrenal insufficiency develops)

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

FDA & Trial Timeline

1 event
Sep 2019Functional Endoscopic Sinus Surgery Study

University of Florida — PHASE1, PHASE2

TrialACTIVE NOT RECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Bilateral massive adrenal hemorrhage.

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No actively recruiting trials found for Bilateral massive adrenal hemorrhage at this time.

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No specialists are currently listed for Bilateral massive adrenal hemorrhage.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

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Latest news about Bilateral massive adrenal hemorrhage

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Caregiver Resources

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Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What caused the adrenal hemorrhage in my case, and can that cause be treated or prevented from recurring?,What are the exact doses and timing for my hormone replacement medications?,How do I adjust my medication during illness, surgery, or physical stress?,Can you teach me or my family how to give an emergency hydrocortisone injection?,What symptoms should prompt me to go to the emergency room immediately?,Will I need to see an endocrinologist for the rest of my life, and how often?,Are there any medications, supplements, or activities I should avoid?

Common questions about Bilateral massive adrenal hemorrhage

What is Bilateral massive adrenal hemorrhage?

Bilateral massive adrenal hemorrhage is a rare and serious condition in which both adrenal glands — small organs that sit on top of each kidney — experience severe bleeding. The adrenal glands produce essential hormones such as cortisol (which helps your body respond to stress) and aldosterone (which helps control blood pressure and salt balance). When both glands are damaged by heavy bleeding, they can no longer make enough of these hormones, leading to a life-threatening condition called acute adrenal insufficiency or adrenal crisis. This condition can be triggered by several factors, inclu

How is Bilateral massive adrenal hemorrhage inherited?

Bilateral massive adrenal hemorrhage follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.