Benign infantile focal epilepsy with midline spikes and waves during sleep

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Overview

Benign infantile focal epilepsy with midline spikes and waves during sleep is a rare type of epilepsy that begins in infancy or early childhood. It is sometimes referred to as benign infantile seizures with midline spikes and waves during sleep. This condition is characterized by focal seizures, which means the abnormal electrical activity in the brain starts in one specific area. A distinctive feature of this epilepsy is the pattern seen on an EEG (brain wave test) during sleep, where spikes and waves appear along the midline of the brain. Children with this condition typically develop normally before and after the onset of seizures. The seizures usually begin between the ages of 3 months and 2 years. Episodes may involve staring, head turning, limb jerking on one side of the body, or brief pauses in activity. Some children may also experience secondary generalization, where the seizure spreads to involve the whole body. The word 'benign' in the name reflects the generally favorable outcome. Most children respond well to standard anti-seizure medications, and many outgrow the seizures entirely by early to mid-childhood. Cognitive development and neurological function typically remain normal. Treatment usually involves anti-epileptic drugs to control seizures during the active phase of the condition, and medication can often be gradually withdrawn once the child has been seizure-free for a period of time.

Also known as:

Key symptoms:

Focal seizures (seizures starting in one part of the brain)Head turning to one side during a seizureJerking movements on one side of the bodyStaring spells or brief pauses in activityAbnormal brain wave patterns during sleepOccasional whole-body seizuresBrief episodes of unresponsivenessEye deviation to one side during a seizureFlushing or color changes during a seizureClusters of seizures occurring over a short period

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Infantile

Begins in infancy, roughly 1 month to 2 years old

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Benign infantile focal epilepsy with midline spikes and waves during sleep.

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No specialists are currently listed for Benign infantile focal epilepsy with midline spikes and waves during sleep.

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Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

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Community

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Caregiver Resources

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Questions for your doctor

Bring these to your next appointment

  • Q1.How certain are you that this is a benign form of epilepsy, and what tests confirm this?,Which anti-seizure medication do you recommend, and what are the possible side effects?,How often will my child need EEG monitoring or follow-up visits?,At what point can we consider tapering off the medication?,Should my child have genetic testing, and what would the results mean for our family?,What should I do if my child has a seizure at home — when should I call an ambulance?,Will this condition affect my child's development or ability to attend school normally?

Common questions about Benign infantile focal epilepsy with midline spikes and waves during sleep

What is Benign infantile focal epilepsy with midline spikes and waves during sleep?

Benign infantile focal epilepsy with midline spikes and waves during sleep is a rare type of epilepsy that begins in infancy or early childhood. It is sometimes referred to as benign infantile seizures with midline spikes and waves during sleep. This condition is characterized by focal seizures, which means the abnormal electrical activity in the brain starts in one specific area. A distinctive feature of this epilepsy is the pattern seen on an EEG (brain wave test) during sleep, where spikes and waves appear along the midline of the brain. Children with this condition typically develop norma

At what age does Benign infantile focal epilepsy with midline spikes and waves during sleep typically begin?

Typical onset of Benign infantile focal epilepsy with midline spikes and waves during sleep is infantile. Age of onset can vary across affected individuals.