Autism spectrum disorder-epilepsy-arthrogryposis syndrome

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ORPHA:370943OMIM:615553Q87.8
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Overview

Autism spectrum disorder-epilepsy-arthrogryposis syndrome is an extremely rare genetic condition that affects multiple body systems, primarily the brain and joints. The syndrome combines three main features: autism spectrum disorder (which affects social communication and behavior), epilepsy (recurrent seizures), and arthrogryposis (joint contractures present at birth that limit movement in two or more joints). Children born with this condition typically show signs from birth or early infancy. The arthrogryposis causes stiff, curved joints that may affect the arms, legs, or both, making movement difficult. Epilepsy can range from mild to severe and may be difficult to control with standard seizure medications. The autism spectrum disorder component affects how the child communicates, interacts socially, and behaves, often including intellectual disability of varying degrees. This syndrome is caused by genetic changes and is classified under the broader category of multiple congenital anomaly syndromes (ICD-10 code Q87.8). Because this condition is so rare, treatment is mainly supportive and tailored to each individual's specific symptoms. A team of specialists is usually needed to manage the different aspects of the disease, including neurologists for seizures, developmental specialists for autism, and orthopedic doctors for joint problems.

Also known as:

Key symptoms:

Joint stiffness and contractures present at birthSeizures or epilepsyAutism spectrum disorderIntellectual disabilityDelayed speech and language developmentDelayed motor milestones like sitting and walkingDifficulty with social interactionRepetitive behaviorsLimited range of motion in arms or legsMuscle weakness or wastingFeeding difficulties in infancyLow muscle tone

Clinical phenotype terms (10)— hover any for plain English
Knee dislocationHP:0004976HammertoeHP:0001765Generalized non-motor (absence) seizureHP:0002121
Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Autism spectrum disorder-epilepsy-arthrogryposis syndrome.

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No actively recruiting trials found for Autism spectrum disorder-epilepsy-arthrogryposis syndrome at this time.

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Search ClinicalTrials.gov ↗Join the Autism spectrum disorder-epilepsy-arthrogryposis syndrome community →

No specialists are currently listed for Autism spectrum disorder-epilepsy-arthrogryposis syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Autism spectrum disorder-epilepsy-arthrogryposis syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Autism spectrum disorder-epilepsy-arthrogryposis syndrome

2 articles
Clinical trialUNITERAREApr 4, 2026
New Recruiting Trial: TF-CBT for Autistic Youth Pilot Implementation - Open Pilot
Researchers at Dartmouth-Hitchcock Medical Center are testing a therapy called TF-CBT (Trauma-Focused Cognitive Behavioral Therapy) to see if it works well for
Clinical trialUNITERAREApr 3, 2026
New Recruiting Trial: Transcranial Direct Current Stimulation in Children With Autism
Researchers at New York State Institute for Basic Research are testing a new treatment called transcranial direct current stimulation (tDCS) in children with au
See all news about Autism spectrum disorder-epilepsy-arthrogryposis syndrome

Caregiver Resources

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Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific genetic change is causing my child's condition, and what does it mean for our family?,What types of seizures does my child have, and what is the best medication to control them?,What therapies are recommended to help with joint mobility and motor development?,What early intervention services should we start for autism and developmental delays?,Are there any clinical trials or research studies we should know about?,What should I do if my child has a prolonged seizure at home?,How often should my child be seen by each specialist on the care team?

Common questions about Autism spectrum disorder-epilepsy-arthrogryposis syndrome

What is Autism spectrum disorder-epilepsy-arthrogryposis syndrome?

Autism spectrum disorder-epilepsy-arthrogryposis syndrome is an extremely rare genetic condition that affects multiple body systems, primarily the brain and joints. The syndrome combines three main features: autism spectrum disorder (which affects social communication and behavior), epilepsy (recurrent seizures), and arthrogryposis (joint contractures present at birth that limit movement in two or more joints). Children born with this condition typically show signs from birth or early infancy. The arthrogryposis causes stiff, curved joints that may affect the arms, legs, or both, making moveme

How is Autism spectrum disorder-epilepsy-arthrogryposis syndrome inherited?

Autism spectrum disorder-epilepsy-arthrogryposis syndrome follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Autism spectrum disorder-epilepsy-arthrogryposis syndrome typically begin?

Typical onset of Autism spectrum disorder-epilepsy-arthrogryposis syndrome is neonatal. Age of onset can vary across affected individuals.