Autism spectrum disorder due to AUTS2 deficiency

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ORPHA:352490OMIM:615834F84.1
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Overview

Autism spectrum disorder due to AUTS2 deficiency is a rare genetic condition caused by changes (mutations or deletions) in the AUTS2 gene, which plays an important role in brain development. This condition is sometimes called AUTS2 syndrome or AUTS2 deficiency syndrome. It affects how the brain grows and functions, leading to a range of developmental and behavioral challenges. Children with this condition typically show signs of autism spectrum disorder, which means they may have difficulty with social communication, repetitive behaviors, and restricted interests. In addition, many affected individuals experience intellectual disability that can range from mild to moderate, delayed speech and language development, and delays in reaching motor milestones like sitting and walking. Some children also have distinctive facial features, feeding difficulties in infancy, and a smaller-than-average head size (microcephaly). Growth may also be affected, with some children being shorter than expected for their age. There is currently no cure for AUTS2 deficiency. Treatment focuses on managing symptoms and supporting development through early intervention programs, speech therapy, occupational therapy, behavioral therapy, and special education services. Some individuals may benefit from medications to manage specific behavioral symptoms such as anxiety, attention difficulties, or irritability. With appropriate support, many individuals can make meaningful developmental progress, though the degree of improvement varies from person to person.

Also known as:

Key symptoms:

Autism spectrum behaviors such as difficulty with social interactionIntellectual disability (mild to moderate)Delayed speech and language developmentDelayed motor milestones like sitting and walkingSmaller-than-average head size (microcephaly)Short stature or growth delaysFeeding difficulties in infancyLow muscle tone (feeling floppy)Attention difficulties or hyperactivityRepetitive behaviors or restricted interestsDistinctive facial features such as a narrow face or prominent foreheadAnxiety or emotional regulation difficultiesLearning difficultiesSeizures in some individuals

Clinical phenotype terms (50)— hover any for plain English
Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Infantile

Begins in infancy, roughly 1 month to 2 years old

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Autism spectrum disorder due to AUTS2 deficiency.

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No actively recruiting trials found for Autism spectrum disorder due to AUTS2 deficiency at this time.

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Specialists

2 foundView all specialists →

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Autism spectrum disorder due to AUTS2 deficiency.

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Community

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Latest news about Autism spectrum disorder due to AUTS2 deficiency

2 articles
Clinical trialUNITERAREApr 4, 2026
New Recruiting Trial: TF-CBT for Autistic Youth Pilot Implementation - Open Pilot
Researchers at Dartmouth-Hitchcock Medical Center are testing a therapy called TF-CBT (Trauma-Focused Cognitive Behavioral Therapy) to see if it works well for
Clinical trialUNITERAREApr 3, 2026
New Recruiting Trial: Transcranial Direct Current Stimulation in Children With Autism
Researchers at New York State Institute for Basic Research are testing a new treatment called transcranial direct current stimulation (tDCS) in children with au
See all news about Autism spectrum disorder due to AUTS2 deficiency

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific genetic change was found in my child's AUTS2 gene, and what does it mean for their development?,What therapies should we start right away, and how often should they occur?,Are there any medications that might help with my child's specific symptoms?,Should my child be monitored for seizures or other medical complications?,What educational supports and accommodations should we request at school?,Is there a risk that future children could also have this condition, and should we see a genetic counselor?,Are there any clinical trials or research studies we should know about?

Common questions about Autism spectrum disorder due to AUTS2 deficiency

What is Autism spectrum disorder due to AUTS2 deficiency?

Autism spectrum disorder due to AUTS2 deficiency is a rare genetic condition caused by changes (mutations or deletions) in the AUTS2 gene, which plays an important role in brain development. This condition is sometimes called AUTS2 syndrome or AUTS2 deficiency syndrome. It affects how the brain grows and functions, leading to a range of developmental and behavioral challenges. Children with this condition typically show signs of autism spectrum disorder, which means they may have difficulty with social communication, repetitive behaviors, and restricted interests. In addition, many affected i

How is Autism spectrum disorder due to AUTS2 deficiency inherited?

Autism spectrum disorder due to AUTS2 deficiency follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Autism spectrum disorder due to AUTS2 deficiency typically begin?

Typical onset of Autism spectrum disorder due to AUTS2 deficiency is infantile. Age of onset can vary across affected individuals.

Which specialists treat Autism spectrum disorder due to AUTS2 deficiency?

2 specialists and care centers treating Autism spectrum disorder due to AUTS2 deficiency are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.