Arachnodactyly-abnormal ossification-intellectual disability syndrome

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ORPHA:1129Q87.8
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Overview

Arachnodactyly-abnormal ossification-intellectual disability syndrome is an extremely rare genetic condition that affects multiple body systems. The name describes its three main features: arachnodactyly (unusually long, slender fingers and toes that resemble spider legs), abnormal ossification (problems with how bones form and harden), and intellectual disability (difficulties with learning and thinking skills). This condition is sometimes also referred to by its Orphanet designation ORPHA:1129. Because this syndrome is so rare, only a very small number of cases have been described in the medical literature. Affected individuals typically show skeletal abnormalities that are noticeable from birth or early childhood, including the characteristic long fingers and toes, along with unusual bone development. Intellectual disability can range from mild to more significant, affecting a child's ability to reach developmental milestones at typical ages. There is currently no cure for this condition. Treatment focuses on managing individual symptoms and may include physical therapy, occupational therapy, special education support, and regular monitoring of bone and skeletal health. A team of specialists typically works together to provide the best care for affected individuals.

Also known as:

Key symptoms:

Unusually long and slender fingers and toesAbnormal bone formation and hardeningIntellectual disability or learning difficultiesDelayed developmental milestonesJoint looseness or hypermobilitySkeletal abnormalitiesUnusual facial featuresShort stature or growth delaysThin body buildDelayed speech development

Clinical phenotype terms (15)— hover any for plain English
Shallow orbitsHP:0000586Thin calvariumHP:0010539Aplasia/Hypoplasia of the EpiglottisHP:0010565
Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Arachnodactyly-abnormal ossification-intellectual disability syndrome.

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No actively recruiting trials found for Arachnodactyly-abnormal ossification-intellectual disability syndrome at this time.

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No specialists are currently listed for Arachnodactyly-abnormal ossification-intellectual disability syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Arachnodactyly-abnormal ossification-intellectual disability syndrome.

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Community

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Caregiver Resources

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Social Security Disability

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Questions for your doctor

Bring these to your next appointment

  • Q1.What specific tests can help confirm this diagnosis in my child?,Should we pursue whole exome or whole genome sequencing to look for the genetic cause?,What therapies should we start right away to support my child's development?,How often should my child have skeletal or bone health evaluations?,What is the expected range of intellectual disability, and how can we best support learning?,Are there any clinical trials or research studies we could participate in?,What is the chance of having another child with the same condition?

Common questions about Arachnodactyly-abnormal ossification-intellectual disability syndrome

What is Arachnodactyly-abnormal ossification-intellectual disability syndrome?

Arachnodactyly-abnormal ossification-intellectual disability syndrome is an extremely rare genetic condition that affects multiple body systems. The name describes its three main features: arachnodactyly (unusually long, slender fingers and toes that resemble spider legs), abnormal ossification (problems with how bones form and harden), and intellectual disability (difficulties with learning and thinking skills). This condition is sometimes also referred to by its Orphanet designation ORPHA:1129. Because this syndrome is so rare, only a very small number of cases have been described in the me

How is Arachnodactyly-abnormal ossification-intellectual disability syndrome inherited?

Arachnodactyly-abnormal ossification-intellectual disability syndrome follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Arachnodactyly-abnormal ossification-intellectual disability syndrome typically begin?

Typical onset of Arachnodactyly-abnormal ossification-intellectual disability syndrome is neonatal. Age of onset can vary across affected individuals.