Angora hair nevus

Angora hair nevus is an extremely rare benign cutaneous hamartoma characterized by a well-circumscribed patch of skin from which unusually long, fine, soft, and white or lightly pigmented hair grows, resembling the silky texture of Angora rabbit or goat hair. The condition primarily affects the skin and its appendages (hair follicles). The nevus typically presents as a solitary lesion, most commonly on the trunk or extremities, and is usually noted in childhood. The abnormal hair within the lesion grows significantly longer and finer than surrounding normal hair, giving it a distinctive fluffy or downy appearance. Angora hair nevus is considered a form of hair follicle hamartoma and falls under the broader category of epidermal and appendageal nevi. It is classified under ICD-10 code Q82.5 (congenital non-neoplastic nevus). The condition is benign and does not carry a risk of malignant transformation. It is generally an isolated finding without systemic associations, though rare reports have described it in the context of other cutaneous anomalies. No specific treatment is required unless desired for cosmetic reasons, in which case options may include simple excision, laser hair removal, or periodic trimming of the affected hair. The condition does not affect overall health or life expectancy.

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