Angiostrongyliasis

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1FDA treatments31Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Angiostrongyliasis is an infection caused by parasitic roundworms called Angiostrongylus. There are two main forms of this disease. The first, caused by Angiostrongylus cantonensis, mainly affects the brain and spinal cord and is sometimes called rat lungworm disease or eosinophilic meningitis. The second, caused by Angiostrongylus costaricensis, affects the intestines and abdomen and is sometimes called abdominal angiostrongyliasis. People usually get infected by accidentally eating raw or undercooked snails, slugs, freshwater shrimp, crabs, or vegetables contaminated with larvae from these parasites. Rats are the natural host of the worm, and snails or slugs pick up the larvae from rat droppings. When the brain form occurs, the larvae travel to the brain and cause inflammation of the membranes surrounding the brain and spinal cord. This leads to severe headaches, stiff neck, nausea, vomiting, and sometimes tingling or pain in the skin. In the abdominal form, the worms cause inflammation in the gut wall, leading to stomach pain, fever, and sometimes a lump in the belly. Most people with the brain form recover fully, though recovery can take weeks to months. Severe cases can cause lasting nerve damage or, rarely, death. Treatment focuses on relieving symptoms, reducing inflammation with steroids, and sometimes using antiparasitic medicines. There is no vaccine to prevent this infection.

Key symptoms:

Severe headacheStiff neckNausea and vomitingTingling, burning, or unusual skin sensationsSensitivity to lightFeverFatigue and general weaknessStomach or abdominal pain (abdominal form)Swollen or tender belly (abdominal form)Diarrhea or constipation (abdominal form)Blurred or double vision (in severe brain cases)Muscle achesLow-grade fever

Clinical phenotype terms (39)— hover any for plain English
CSF pleocytosisHP:0012229Severely increased total eosinophil countHP:0032061Projectile vomitingHP:0002587Unusual CNS infectionHP:0011450Stiff neckHP:0025258
Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

Treatments

1 available

Azithromycin

AZITHROMYCIN· Preferred Pharmaceuticals Inc.

Pharyngitis/tonsillitis in adults and pediatric patients (2 years of age and older)

No actively recruiting trials found for Angiostrongyliasis at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Angiostrongyliasis community →

Specialists

Showing 25 of 31View all specialists →
RR
Rubens Rodriguez
Specialist
4 Angiostrongyliasis publications
AR
Alicia Rojas
Specialist
4 Angiostrongyliasis publications
JM
Javier Mora
ORANGEVALE, CA
Specialist
2 Angiostrongyliasis publications
AS
Alberto Solano-Barquero
Specialist
2 Angiostrongyliasis publications
KC
Ke-Min Chen
Specialist
2 Angiostrongyliasis publications
SL
Shih-Chan Lai
Specialist
2 Angiostrongyliasis publications
PR
Phoebe Rivory
Specialist
2 Angiostrongyliasis publications
RL
Rogan Lee
Specialist
2 Angiostrongyliasis publications
MW
Michael P Ward
Specialist
2 Angiostrongyliasis publications
J&
Jan Šlapeta
Specialist
2 Angiostrongyliasis publications
PB
Patcharaporn Boonroumkaew
Specialist
2 Angiostrongyliasis publications
LS
Lakkhana Sadaow
Specialist
2 Angiostrongyliasis publications
RR
Rutchanee Rodpai
Specialist
2 Angiostrongyliasis publications
OS
Oranuch Sanpool
Specialist
2 Angiostrongyliasis publications
CG
Carlos Graeff-Teixeira
Specialist
5 Angiostrongyliasis publications
ND
Nicole DESBOIS
Specialist
PI on 1 active trial
YC
Yi-Ju Chen
TORRANCE, CA
Specialist
3 Angiostrongyliasis publications
LW
Lian-Chen Wang
Specialist
6 Angiostrongyliasis publications
KC
Kuang-Yao Chen
Specialist
5 Angiostrongyliasis publications
KJ
Kai-Yuan Jhan
Specialist
4 Angiostrongyliasis publications
CC
Chien-Ju Cheng
Specialist
4 Angiostrongyliasis publications
CC
Cheng-Hsun Chiu
Specialist
3 Angiostrongyliasis publications
DM
David Modry
Specialist
2 Angiostrongyliasis publications
CP
Claudia Paredes-Esquivel
Specialist
2 Angiostrongyliasis publications
CL
Cheng-You Lu
Specialist
2 Angiostrongyliasis publications

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Angiostrongyliasis.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Angiostrongyliasis

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Do I need a spinal tap, and how will the results guide my treatment?,Should I take antiparasitic medication, and what are the risks and benefits?,How long will my symptoms last, and what is my expected recovery timeline?,Are there any lasting complications I should watch for after I recover?,What warning signs should prompt me to go to the emergency room?,Is there anything I can do to speed up my recovery at home?,How can I prevent getting this infection again in the future?

Common questions about Angiostrongyliasis

What is Angiostrongyliasis?

Angiostrongyliasis is an infection caused by parasitic roundworms called Angiostrongylus. There are two main forms of this disease. The first, caused by Angiostrongylus cantonensis, mainly affects the brain and spinal cord and is sometimes called rat lungworm disease or eosinophilic meningitis. The second, caused by Angiostrongylus costaricensis, affects the intestines and abdomen and is sometimes called abdominal angiostrongyliasis. People usually get infected by accidentally eating raw or undercooked snails, slugs, freshwater shrimp, crabs, or vegetables contaminated with larvae from these p

How is Angiostrongyliasis inherited?

Angiostrongyliasis follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

Which specialists treat Angiostrongyliasis?

25 specialists and care centers treating Angiostrongyliasis are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.