Ameloblastoma

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19Specialists8Treatment centers

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Overview

Ameloblastoma is a rare, usually slow-growing tumor that develops in the jawbone, most commonly in the lower jaw (mandible) near the back teeth. The name comes from 'ameloblasts,' which are the cells that form tooth enamel during development. Although ameloblastoma is classified as a benign (non-cancerous) tumor, it behaves aggressively by growing into surrounding bone and tissue, which makes it locally destructive if left untreated. In very rare cases, it can become malignant (cancerous) and spread to other parts of the body. The most common symptoms include a painless swelling or lump in the jaw that gradually gets bigger over time. As the tumor grows, it can cause facial deformity, loose teeth, difficulty chewing, and sometimes numbness or tingling in the jaw area. Many people first notice the tumor when a dentist finds an unusual area on a routine X-ray. The main treatment for ameloblastoma is surgery to remove the tumor along with a margin of healthy bone to reduce the chance of it coming back. Smaller or less aggressive types may be treated with a more conservative approach, such as scraping out the tumor (curettage). After surgery, reconstructive procedures may be needed to restore the jawbone and improve appearance and function. Radiation therapy is sometimes used when surgery is not possible or when the tumor returns. Because ameloblastoma has a notable tendency to recur, long-term follow-up with regular imaging is very important.

Key symptoms:

Painless swelling in the jawGradually enlarging lump in the lower jawFacial asymmetry or deformityLoose or displaced teethDifficulty chewing or opening the mouthNumbness or tingling in the jaw or chinPain in the jaw (in advanced cases)A mass felt inside the mouthDifficulty fitting denturesAbnormal findings on dental X-raysTooth that fails to come in properlyNasal obstruction (if upper jaw is involved)

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Ameloblastoma.

View clinical trials →

No actively recruiting trials found for Ameloblastoma at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Ameloblastoma community →

Specialists

19 foundView all specialists →
GX
Gan Xiong
Specialist
2 Ameloblastoma publications
SK
Shosei Kishida
Specialist
2 Ameloblastoma publications
CW
Cheng Wang
Specialist
2 Ameloblastoma publications
NN
Norifumi Nakamura
Specialist
2 Ameloblastoma publications
YO
Yusuke Ono
Specialist
2 Ameloblastoma publications
TF
Takao Fuchigami
Specialist
2 Ameloblastoma publications
WC
Wei Cao
Specialist
2 Ameloblastoma publications
CP
CAO Wei, PHD;MD
Specialist
PI on 1 active trial
AC
Alexander Colevas
PALO ALTO, CA
Specialist
PI on 2 active trials1 Ameloblastoma publication
YP
yehia A El-Mahallawy, PhD
Specialist
PI on 1 active trial
TL
TAREK ABDELBARY, Lecturer
Specialist
PI on 1 active trial
SR
Sushil Rayamajhi
PENSACOLA, FL
Specialist
1 Ameloblastoma publication
SG
Suhani Ghai
Specialist
1 Ameloblastoma publication
SS
Samata Shakya
Specialist
1 Ameloblastoma publication
KS
Kopila Shahi
Specialist
1 Ameloblastoma publication
SB
Sagar Bhandari
BROOKLYN, NY
Specialist
1 Ameloblastoma publication
XL
X-H Liu
Specialist
1 Ameloblastoma publication
AT
Anu Radha Twayana
ODESSA, TX
Specialist
1 Ameloblastoma publication
SS
Sunita Shrestha
BRONX, NY
Specialist
1 Ameloblastoma publication

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Ameloblastoma.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Ameloblastoma

No recent news articles for Ameloblastoma.

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What type of ameloblastoma do I have, and how does that affect my treatment options?,What surgical approach do you recommend, and what are the risks and benefits?,Will I need reconstructive surgery, and what will that involve?,What is the chance that the tumor will come back after treatment?,How often will I need follow-up imaging, and for how long?,Are there any clinical trials or targeted therapies that might be appropriate for my case?,How will treatment affect my ability to eat, speak, and go about my daily life?

Common questions about Ameloblastoma

What is Ameloblastoma?

Ameloblastoma is a rare, usually slow-growing tumor that develops in the jawbone, most commonly in the lower jaw (mandible) near the back teeth. The name comes from 'ameloblasts,' which are the cells that form tooth enamel during development. Although ameloblastoma is classified as a benign (non-cancerous) tumor, it behaves aggressively by growing into surrounding bone and tissue, which makes it locally destructive if left untreated. In very rare cases, it can become malignant (cancerous) and spread to other parts of the body. The most common symptoms include a painless swelling or lump in th

How is Ameloblastoma inherited?

Ameloblastoma follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Ameloblastoma typically begin?

Typical onset of Ameloblastoma is adult. Age of onset can vary across affected individuals.

Which specialists treat Ameloblastoma?

19 specialists and care centers treating Ameloblastoma are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.