Acquired porencephaly

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5Specialists8Treatment centers

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Overview

Acquired porencephaly is a condition in which fluid-filled cavities (cysts) form in the brain. Unlike congenital (inborn) porencephaly, the acquired form develops after birth due to damage to brain tissue. This damage is most often caused by events such as a stroke, infection, head trauma, or complications during or shortly after birth that interrupt blood flow to parts of the brain. When brain tissue is destroyed, the body replaces it with fluid-filled spaces that connect to the brain's normal fluid-filled chambers (ventricles) or to the surface of the brain. The symptoms of acquired porencephaly vary widely depending on the size and location of the cyst. Common problems include seizures, muscle weakness or paralysis on one side of the body (hemiparesis), delays in reaching developmental milestones, intellectual disability, speech and language difficulties, and vision problems. Some individuals have mild symptoms, while others are severely affected. There is no cure for acquired porencephaly. Treatment focuses on managing symptoms and supporting development. This may include anti-seizure medications, physical therapy, occupational therapy, speech therapy, and in some cases surgery to relieve pressure in the brain if the cyst grows or causes increased intracranial pressure. Early intervention with therapies can help children reach their best possible developmental outcomes. A team of specialists typically works together to provide comprehensive care.

Key symptoms:

Seizures or epilepsyWeakness or paralysis on one side of the bodyDelayed developmental milestonesIntellectual disabilitySpeech and language delaysVision problemsDifficulty with movement and coordinationLearning difficultiesMuscle stiffness or spasticityHeadachesFeeding difficulties in infantsBehavioral challengesReduced head growth in infants

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Acquired porencephaly.

View clinical trials →

No actively recruiting trials found for Acquired porencephaly at this time.

New trials open frequently. Follow this disease to get notified.

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Specialists

5 foundView all specialists →
MP
Maria Gabriela Puiu
Specialist
1 Acquired porencephaly publication
VD
Vlad Dionisie
Specialist
1 Acquired porencephaly publication
AF
Alexandru Cristian Filip
Specialist
1 Acquired porencephaly publication
MM
Mirela Manea
Specialist
1 Acquired porencephaly publication
HM
Hugues CHABRIAT, MD,PhD
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Acquired porencephaly.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Acquired porencephaly

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is the size and location of the brain cyst, and how does that affect my child's specific symptoms?,What caused the brain injury that led to porencephaly, and could it happen again?,What seizure medications do you recommend, and what are the possible side effects?,What therapies (physical, occupational, speech) should we start, and how often?,Are there any signs of hydrocephalus or increased brain pressure that we should watch for?,What is the long-term outlook for development, learning, and independence?,Should we have follow-up brain imaging, and how often?

Common questions about Acquired porencephaly

What is Acquired porencephaly?

Acquired porencephaly is a condition in which fluid-filled cavities (cysts) form in the brain. Unlike congenital (inborn) porencephaly, the acquired form develops after birth due to damage to brain tissue. This damage is most often caused by events such as a stroke, infection, head trauma, or complications during or shortly after birth that interrupt blood flow to parts of the brain. When brain tissue is destroyed, the body replaces it with fluid-filled spaces that connect to the brain's normal fluid-filled chambers (ventricles) or to the surface of the brain. The symptoms of acquired porence

How is Acquired porencephaly inherited?

Acquired porencephaly follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

Which specialists treat Acquired porencephaly?

5 specialists and care centers treating Acquired porencephaly are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.