Acquired kinky hair syndrome

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Overview

Acquired kinky hair syndrome is a rare condition where the hair becomes abnormally twisted, brittle, and kinky — not because of genetics, but because of a deficiency in copper in the body. Unlike the inherited form of kinky hair disease (known as Menkes disease), this acquired version develops after birth due to low copper levels caused by an outside factor, such as poor nutrition, problems absorbing nutrients, or certain medical treatments. Copper is an essential mineral that the body needs to build strong, healthy hair, among many other functions. The most common cause is copper deficiency, which can happen in premature babies receiving intravenous nutrition without enough copper, or in people who have had certain bowel surgeries that reduce nutrient absorption. The hair changes are often the most visible sign, but low copper can also affect the nervous system, bones, and blood. Treatment focuses on correcting the copper deficiency, usually through copper supplements given by mouth or through a vein. When caught early and treated properly, many of the symptoms can improve or even reverse. Regular monitoring by a specialist is important to make sure copper levels return to normal and stay there.

Key symptoms:

Kinky, twisted, or unusually brittle hairHair that breaks easilyPale or washed-out skin color (pallor)Anemia (low red blood cell count causing tiredness and weakness)Bone problems or fracturesNerve damage causing numbness or weakness in the limbsPoor growth or failure to thrive in infantsLow energy and fatigueDifficulty walking or poor coordination

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Acquired kinky hair syndrome.

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No actively recruiting trials found for Acquired kinky hair syndrome at this time.

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No specialists are currently listed for Acquired kinky hair syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Acquired kinky hair syndrome.

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Community

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Caregiver Resources

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Questions for your doctor

Bring these to your next appointment

  • Q1.What is causing my copper deficiency, and how do we fix the root cause?,How long will I need to take copper supplements, and how will we know when levels are back to normal?,Will my hair and other symptoms fully recover, or could some damage be permanent?,Do I need to make any changes to my diet to prevent this from happening again?,How often should I have blood tests to monitor my copper levels?,Are there any risks or side effects from taking copper supplements?,Should other family members be tested, or is this condition not inherited?

Common questions about Acquired kinky hair syndrome

What is Acquired kinky hair syndrome?

Acquired kinky hair syndrome is a rare condition where the hair becomes abnormally twisted, brittle, and kinky — not because of genetics, but because of a deficiency in copper in the body. Unlike the inherited form of kinky hair disease (known as Menkes disease), this acquired version develops after birth due to low copper levels caused by an outside factor, such as poor nutrition, problems absorbing nutrients, or certain medical treatments. Copper is an essential mineral that the body needs to build strong, healthy hair, among many other functions. The most common cause is copper deficiency,

How is Acquired kinky hair syndrome inherited?

Acquired kinky hair syndrome follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.