9q31.1q31.3 microdeletion syndrome

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ORPHA:401923Q93.5
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Overview

9q31.1q31.3 microdeletion syndrome is an extremely rare genetic condition caused by a small missing piece (deletion) of chromosome 9 in the region labeled q31.1 to q31.3. This syndrome is sometimes referred to as 9q31 deletion syndrome or chromosome 9q31.1-q31.3 deletion syndrome. Because a section of genetic material is lost, several genes that are important for normal development are affected. Children born with this condition typically show developmental delays, intellectual disability, and distinctive facial features. Many affected individuals have problems with speech and language development, low muscle tone (hypotonia), and feeding difficulties in infancy. Some children may also have heart defects, skeletal abnormalities, or problems with other organ systems. Growth may be slower than expected, and short stature is sometimes observed. Because this syndrome is so rare, there is no specific cure or targeted treatment. Management focuses on addressing each individual's symptoms through therapies such as speech therapy, physical therapy, occupational therapy, and special education support. Heart defects or other structural problems may require surgical intervention. Early intervention programs can help children reach their fullest potential. A team of specialists typically works together to provide comprehensive care tailored to each patient's needs.

Also known as:

Key symptoms:

Intellectual disabilityDelayed speech and language developmentLow muscle tone (floppiness)Distinctive facial featuresFeeding difficulties in infancyShort stature or slow growthDelayed motor milestones such as sitting and walkingHeart defectsSkeletal abnormalitiesBehavioral difficultiesSeizures in some casesSmall head size (microcephaly)Vision or eye problems

Clinical phenotype terms (22)— hover any for plain English
Short claviclesHP:0000894Cervical kyphosisHP:0002947Broad chinHP:0011822OverweightHP:0025502Renovascular hypertensionHP:0100817
Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for 9q31.1q31.3 microdeletion syndrome.

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No actively recruiting trials found for 9q31.1q31.3 microdeletion syndrome at this time.

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No specialists are currently listed for 9q31.1q31.3 microdeletion syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to 9q31.1q31.3 microdeletion syndrome.

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Community

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Caregiver Resources

NORD Caregiver Resources

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Mental Health Support

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Family & Caregiver Grants

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Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is the exact size and location of my child's deletion, and how might that affect their symptoms?,Was this deletion inherited or did it happen spontaneously, and should other family members be tested?,What early intervention therapies should we start right away?,Does my child need a heart evaluation or other organ screening?,What developmental milestones should we watch for, and when should we be concerned?,Are there any clinical studies or research programs we could participate in?,What resources or support groups are available for families with this condition?

Common questions about 9q31.1q31.3 microdeletion syndrome

What is 9q31.1q31.3 microdeletion syndrome?

9q31.1q31.3 microdeletion syndrome is an extremely rare genetic condition caused by a small missing piece (deletion) of chromosome 9 in the region labeled q31.1 to q31.3. This syndrome is sometimes referred to as 9q31 deletion syndrome or chromosome 9q31.1-q31.3 deletion syndrome. Because a section of genetic material is lost, several genes that are important for normal development are affected. Children born with this condition typically show developmental delays, intellectual disability, and distinctive facial features. Many affected individuals have problems with speech and language develo

How is 9q31.1q31.3 microdeletion syndrome inherited?

9q31.1q31.3 microdeletion syndrome follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does 9q31.1q31.3 microdeletion syndrome typically begin?

Typical onset of 9q31.1q31.3 microdeletion syndrome is neonatal. Age of onset can vary across affected individuals.