9q21.13 microdeletion syndrome

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ORPHA:531151Q93.5
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Overview

9q21.13 microdeletion syndrome is a rare genetic condition caused by a tiny missing piece of chromosome 9, in a region called 9q21.13. Because this area of the chromosome contains important genes that help the brain and body develop properly, losing this small segment can cause a range of health and developmental challenges. The condition is also sometimes referred to simply as '9q21.13 deletion syndrome.' Only a small number of people worldwide have been diagnosed with this condition, so doctors are still learning about its full range of effects. The most common features include intellectual disability (difficulty with learning and thinking), delayed speech and language development, and behavioral differences such as autism spectrum disorder or attention difficulties. Many children with this syndrome also have low muscle tone (called hypotonia), which can make it harder to sit, stand, or walk on time. Some individuals may have mild differences in their facial features, and a smaller number may experience seizures. There is currently no cure for 9q21.13 microdeletion syndrome. Treatment focuses on supporting each person's individual needs through therapies such as speech therapy, physical therapy, and occupational therapy. Early intervention programs can make a meaningful difference in helping children reach their potential. A team of specialists typically works together to manage the various aspects of the condition.

Key symptoms:

Intellectual disability (difficulty with learning and thinking)Delayed speech and language developmentLow muscle tone (hypotonia), making movement harderDelayed motor milestones such as sitting, standing, or walking lateAutism spectrum disorder or autistic featuresBehavioral challenges such as hyperactivity or attention difficultiesMild distinctive facial featuresSeizures or epilepsy in some individualsFeeding difficulties in infancyDifficulty with social communication

Clinical phenotype terms (24)— hover any for plain English
Gastrointestinal dysmotilityHP:0002579Inverted nipplesHP:0003186Wide nasal ridgeHP:0012811Abnormal tongue morphologyHP:0030809
Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Infantile

Begins in infancy, roughly 1 month to 2 years old

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for 9q21.13 microdeletion syndrome.

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No actively recruiting trials found for 9q21.13 microdeletion syndrome at this time.

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Search ClinicalTrials.gov ↗Join the 9q21.13 microdeletion syndrome community →

No specialists are currently listed for 9q21.13 microdeletion syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to 9q21.13 microdeletion syndrome.

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Community

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific genes are missing in my child's deletion, and how might that affect their development?,Should other family members be tested for this deletion?,What therapies should we start right away, and how often should my child receive them?,What signs of seizures should I watch for, and what should I do if one happens?,Are there any research studies or patient registries we can join to help advance understanding of this condition?,What educational supports should we request from our school district?,How will my child's needs likely change as they grow into adulthood?

Common questions about 9q21.13 microdeletion syndrome

What is 9q21.13 microdeletion syndrome?

9q21.13 microdeletion syndrome is a rare genetic condition caused by a tiny missing piece of chromosome 9, in a region called 9q21.13. Because this area of the chromosome contains important genes that help the brain and body develop properly, losing this small segment can cause a range of health and developmental challenges. The condition is also sometimes referred to simply as '9q21.13 deletion syndrome.' Only a small number of people worldwide have been diagnosed with this condition, so doctors are still learning about its full range of effects. The most common features include intellectual

At what age does 9q21.13 microdeletion syndrome typically begin?

Typical onset of 9q21.13 microdeletion syndrome is infantile. Age of onset can vary across affected individuals.