1p31p32 microdeletion syndrome

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ORPHA:401986OMIM:613735Q93.5
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8Treatment centers

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Overview

1p31p32 microdeletion syndrome is a very rare genetic condition caused by a small missing piece (microdeletion) of genetic material on the short arm of chromosome 1, specifically in the region between bands p31 and p32. Because this deletion removes several genes at once, it can affect multiple body systems. Children born with this condition typically show developmental delay, meaning they may be slower to reach milestones like sitting, walking, and talking compared to other children their age. Intellectual disability ranging from mild to moderate is common. Many affected individuals also have distinctive facial features, which may include a broad forehead, widely spaced eyes, a flat nasal bridge, and low-set ears. Some children may also experience seizures, behavioral challenges such as autism spectrum features, and problems with growth or feeding in early life. Because this syndrome is so rare, the full range of symptoms is still being understood as more patients are identified. There is currently no cure for 1p31p32 microdeletion syndrome. Treatment focuses on managing individual symptoms and supporting development through therapies such as speech therapy, occupational therapy, and physical therapy. Early intervention services can make a meaningful difference in a child's progress. Seizures, if present, are managed with anti-seizure medications. Regular follow-up with a team of specialists is important to monitor growth, development, and any emerging medical concerns.

Also known as:

Key symptoms:

Developmental delayIntellectual disabilitySpeech and language delaysDistinctive facial featuresSeizures or epilepsyLow muscle tone (floppiness in infancy)Feeding difficulties in infancyGrowth delay or short statureBehavioral challengesAutism spectrum featuresWidely spaced eyesBroad foreheadFlat nasal bridgeLow-set earsMotor skill delays

Clinical phenotype terms (18)— hover any for plain English
Tethered cordHP:0002144Chiari type I malformationHP:0007099Intraventricular hemorrhageHP:0030746Ocular hypertensionHP:0007906Moyamoya phenomenonHP:0011834
Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for 1p31p32 microdeletion syndrome.

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No actively recruiting trials found for 1p31p32 microdeletion syndrome at this time.

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No specialists are currently listed for 1p31p32 microdeletion syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to 1p31p32 microdeletion syndrome.

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Community

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Latest news about 1p31p32 microdeletion syndrome

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is the exact size and location of my child's deletion, and which genes are affected?,Was this deletion inherited or did it happen spontaneously?,What therapies should we start right away to support development?,Should my child be monitored for seizures, and what signs should I watch for?,Are there any other organ systems we should screen, such as the heart or kidneys?,What educational supports or accommodations should we request at school?,Are there any research studies or registries we can participate in?

Common questions about 1p31p32 microdeletion syndrome

What is 1p31p32 microdeletion syndrome?

1p31p32 microdeletion syndrome is a very rare genetic condition caused by a small missing piece (microdeletion) of genetic material on the short arm of chromosome 1, specifically in the region between bands p31 and p32. Because this deletion removes several genes at once, it can affect multiple body systems. Children born with this condition typically show developmental delay, meaning they may be slower to reach milestones like sitting, walking, and talking compared to other children their age. Intellectual disability ranging from mild to moderate is common. Many affected individuals also have

How is 1p31p32 microdeletion syndrome inherited?

1p31p32 microdeletion syndrome follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does 1p31p32 microdeletion syndrome typically begin?

Typical onset of 1p31p32 microdeletion syndrome is neonatal. Age of onset can vary across affected individuals.